alboliras atrioventricular canal defects 11713

Upload: ancaberescu

Post on 02-Jun-2018

225 views

Category:

Documents


0 download

TRANSCRIPT

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    1/57

    !"#$"%& () *+,&+%"-./ 01/ 2*3!/ 2**4/ 2*55

    1%"$67&" &8 2$7-+ 5-"9%&+&:;

    Phoenix Childrens Medical Group Childrens Hospital

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    2/57

    !"#$%&' )*+#%,+$-. /01,-2"&*,0

    / 3"4. 0, 1*0"0#*"% -.%"&*,0+3*5 6*&3 "0' 2"0$1"#&$-.- ,1"0' #,22.-#*"% 5-,)$#& "0)7,- 5-,4*).- ,1 #,22.-#*"%+.-4*#.+ )*+#$++.) *0 &3. 89: "#&*4*&';

    / ), 0,& *0&.0) &, )*+#$++ "0 $0"55-,4.)7*04.+&*;?;@,4.-02.0& A."%&3 /0+$-"0#. B,-&"C*%*&' "0)D##,$0&"C*%*&' D#& ,1 EFFG HA/BDDI 5-*4"#' "0) +.#$-*&'+&"0)"-)+;

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    3/57

    D&-*,4.0&-*#$%"- ?.5&"% J.1.#&+

    :0),#"-)*"% 8$+3*,0 J.1.#&+

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&+

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    4/57

    :2C-',%,

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    5/57

    =3. K,-2"% 8"-)*"# 8-$L

    :*).2M N OPEP

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    6/57

    Characterized by varying degrees ofincomplete development of the septaltissue surrounding the atrioventricular(AV) valves along with varying degrees ofabnormalities of the AV valvesthemselves.

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&+

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    7/57

    8,25%.&. 8,22,0 D&-*,4.0&-*#$%"- 8"0"% !"# %&'( )*+*,'# -. '(* "'/-"0 #*1'23 42#' "%&5* '(* 67 5"05*# 8'-23 1/-323

    69:; ".) )*+*,'# -. '(* 5*.'/-,20"/ #*1'23 42#' %*0&< '(* 67 5"05*#=

    B"-&*"% 8,22,0 D&-*,4.0&-*#$%"- 8"0"% 860#& >.&

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    8/57

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&

    8,$-&.+' ,1 :)6"-)+M S;

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    9/57

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&

    T3M U OPPV

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    10/57

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&+

    :*).2M N OPEP

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    11/57

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&

    8,3.0M 9 OPEP

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    12/57

    @,,+.QK.#W J.1,-2*&' *0 DR 8"0"%

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    13/57

    C&'"0 67? F-'-5* F/*."'"0:*'*,'-&.

    F*/,*.'"A*

    @"-0. OPPE EX EP YGZ

    A.*). H[..)+I OPP\ FO OV OFZ

    ]3,, H? D$+&I OPPX OE Y O^;XZ

    9"-.W OPEP HEFXGQEFFFI

    ^FX EPO OY;GZ

    9"-.W OPEP HOPPPQOPPGI

    EGF E\E X^;\Z

    !-*.)C.-< OPPF E\ G \^Z

    D##$-"#' ,1 >%%&-"+,0,

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    14/57

    D##$-"#' ,1 >%%&-"+,0,

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    15/57

    ?.2C*%*#"% "-&.-' "0) $2C*%*#"% 4.0,$+ 1%,6

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    16/57

    J.&.-2*0"&*,0 ,1 D?J +*a.;

    J.&.-2*0"&*,0 ,1 R?J +*a.;

    D0"&,2' ,1 &3. "&-*,4.0&-*#$%"- "00$%$+M 4"%4.M "0)#3,-)"% "&&"#32.0&+;

    D++.++2.0& 1,- "&-*"% ,- 4.0&-*#$%"- %.4.% $0C"%"0#.;

    D++.++2.0& 1,- [R ,$&1%,6 &-"#& ,C+&-$#&*,0 *1 5-.+.0&;

    A.2,)'0"2*# "++.++2.0& 4"%4"- -.

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    17/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    18/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    19/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    20/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    21/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    22/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    23/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    24/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    25/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    26/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    27/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    28/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    29/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    30/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    31/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    32/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    33/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    34/57

    /2"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    35/57

    ?5,0

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    36/57

    B"-&*"% DR8

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    37/57

    DR8Q&'5. R?J

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    38/57

    DR 8"0"% 6*&3 [RT= TC+&-$#&*,0

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    39/57

    DR 8"0"% 6*&3 =DBR8 &, ?R8

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    40/57

    DR 8"0"% 6*&3 /01-"#"-)*"# =DBR8

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    41/57

    DR 8"0"% 6*&3 =T!

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    42/57

    DR 8"0"% 6*&3 =T!

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    43/57

    DR 8"0"% 6*&3 8,22,0 D&-*$2

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    44/57

    DR 8"0"% 6*&3 ?2"%% [R

    DR 8 7 8,22,0 D&- 8AN ?5,0

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    45/57

    DR 8 67 8,22,0 D&-M 8ANM ?5,0

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    46/57

    [R J,2*0"0& 88DR8

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    47/57

    bR J,2*0"0& 88DR8

    /25,-&"0#. ,1 8,--.#&%' /).0&*1'*0< &3.

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    48/57

    /25,-&"0#. ,1 8,--.#&%' /).0&*1'*0< &3.B-.+.0#. ,1 DR8 J.1.#&

    N.-

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    49/57

    8AJ *0 \XV !.&$+.+ 6*&3 J,60 ?'0)-,2.

    9,

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    50/57

    D++,#*"&.) #,0)*&*,0+ "0) ,$,2. *0 O\G 5-.0"&"%%'

    )*"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    51/57

    D++,#*"&.) #,0)*&*,0+ *0 B"-&*"% DR8

    B"%")*0*M .& "% OPPF

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    52/57

    B-,

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    53/57

    D++,#*"&.) *0&-"#"-)*"# %.+*,0

    D++,#*"&.) .L&-"#"-)*"# +&-$#&$-"%1.&"% %.+*,0

    D++,#*"&.)

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    54/57

    D #,25-.3.0+*4. )*"

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    55/57

    =ADK] dT>e

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    56/57

    =ADK] dT>e

  • 8/11/2019 Alboliras Atrioventricular Canal Defects 11713

    57/57

    D&-*,4.0&-*#$%"- ?.5&"% J.1.#&+

    :0),#"-)*"% 8$+3*,0 J.1.#&+

    D&-*,4.0&-*#$%"- 8"0"% J.1.#&+