american thoracic society international conference …

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Dallas, TXMay 17 - May 22, 2019conference.thoracic.org

Where today’s science meets tomorrow’s careTM

AMERICAN THORACIC SOCIETY INTERNATIONAL CONFERENCE

Rare Lung Disease Guide

May 2019Dear Colleagues:The scope of the American Thoracic Society is amazingly broad — covering pulmonary, critical care, and sleep medicine. The challenge that we face each year as we put the International Conference program together is that some clinical topics that may be of central importance to our members, conference attendees and patients may not be prominently featured in the program. This is especially the case with some rare lung diseases.With each challenge though, comes opportunity. Because of the wealth of scientific and clinical information presented at ATS 2019, these diseases, though uncommon, will be the focus of many presentations over the next several days. The purpose of this Rare Lung Disease Guide is to help you more easily find these presentations.In his chapter on rare lung diseases in “Breathing in America: Diseases, Progress, and Hope” (2010) Francis X. McCormack, MD noted that research on uncommon respiratory diseases has produced some of the most exciting discoveries in pulmonary medicine, stating that “Insights gained from uncommon lung diseases often shed light on the more common ones.”The definition of a rare disease by its prevalence varies by country. In the European Union, for instance, it is defined as a disease that affects fewer than 1 in 2,000 while in the United States it is a disease that affects fewer than 1 in 200,000. This guide was compiled by a small group of ATS Members who studied the ATS 2019 abstracts — authors requested to be considered for inclusion. Many thanks to Dr. Nishant Gupta, Dr. Jonathan Kropski, Dr. Lisa Young, Dr. Cormac McCarthy, and Dr. Justin Hewlett for their assistance with this resource. There are a number of patient advocacy groups that are exhibiting at ATS 2019. In addition to attending the presentations noted within, I encourage you to visit with them to learn more about these rare conditions. Groups listed in BOLD are members of the ATS Public Advisory Roundtable and can all be found in or near PAR PATH, near the ATS Center in the Exhibit Hall. Learn more about this group and its many contributions to the Society and its work at: www.thoracic.org/patients/par/.

Sincerely,Jess Mandel, MD Chair, ATS International Conference Committee

Jess Mandel, MDChair, ATS International Conference Committee

Alpha-1 Foundation: Booth 3021Allergy and Asthma Network: Booth 2916ARDS Foundation: Booth 2823Children’s Interstitial Lung Disease Foundation, Inc. (CHILD): Booth 2816Foundation for Sarcoidosis Research: Booth 2921Hermansky-Pudlak Syndrome Network, Inc.: Booth 2915The LAM Foundation/Lymphangioleiomyomatosis: Booth 2820

Lung Transplant Foundation: Booth 2817LUNGevity Foundation: Booth 2923NTM Info & Research, Inc.: Booth 2815Primary Ciliary Dyskinesia Foundation (PCD): Booth 2920Pulmonary Fibrosis Foundation: Booth 3126Scleroderma Foundation: Booth 2917Tuberous Sclerosis Alliance: Booth 2821

List Current as of 4/2/19

DISCLAIMERThe purpose of this guide is to help the American Thoracic Society International Conference attendees navigate the viewing of posters for disorders that typically get less attention at the conference because of their rarity. During abstract submission, authors were instructed to check the box for consideration in the Rare Lung Disease Guide; the abstracts on that list were then further narrowed down. Conditions represented by less than 50 abstracts were considered for inclusion. We regret that not all rare diseases could be represented, and welcome suggestions for additional categories for listing in future editions. Please email us with any suggestions: [email protected].

3

Rare Disease Term

Date/Day Board Number/Time Abstract Title Session ID and Title Location

ADULT

ADULT

AMYLOIDOSIS

Sunday, May 19, 2019

P557 9:15 am-4:15 pm Sarcoloidosis: A Rare Case Of Co-Existent Systemic Sarcoidosis And Amyloidosis A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P1005 9:15 am-4:15 pm A Case Of Fatal Respiratory Failure Caused By Diaphragmatic Amyloidosis A48: CRITICAL CARE CASE REPORTS: CAUSES AND COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Area G (Hall F, Level 2), KBHCCD

Monday, May 20, 2019

P295 9:15 am-4:15 pm Rare Cause Of Chronic Cough From Pulmonary Amyloidosis B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P383 9:15 am-4:15 pm Primary Pleural Amyloidosis With Isolated Endobronchial Lesion B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

Tuesday, May 21, 2019

P507 9:15 am-4:15 pm Amyloidosis Diagnosed By Endobronchial Ultrasound-Guided Transbronchial Needle Aspirate C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

Wednesday, May 22, 2019

P430 9:15 am-3:30 pm Heart-Lung-Kidney Transplantation For Transthyretin (TTR)-Related Hereditary Amyloidosis

D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P502 9:15 am-3:30 pm Hiding In Plain Sight D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P494 9:15 am-3:30 pm A Unique Case Of Diffuse Alveolar-Septal Pulmonary Amyloidosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P493 9:15 am-3:30 pm Amyloid Lung: A Rare Entity Of Pulmonary Nodule D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P567 9:15 am-3:30 pm A Case Report Of Tracheo-Bronchial Amyloidosis D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P619 9:15 am-3:30 pm Persistent Pulmonary Pleural Effusions In A Patient With Systemic Amyloidosis D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

AV MALFORMATION


P842 11:15 am-1:00 pm Platypnea Orthodeoxia Syndrome Following A Submassive Pulmonary Embolism A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD


P296 11:15 am-1:00 pm Hemoptysis Due To A Bleeding Bronchial Dieulafoy Lesion Treated Successfully With Arterial Embolization And Argon Plasma Coagulation B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P951 11:15 am-1:00 pm Anomalous Descending Aorta To Pulmonary Vein Fistula: A Rare Clinical Entity B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

4

Rare Disease Term


ADULT

ADULT


P964 11:15 am-1:00 pm Hemothorax Secondary To Pulmonary AVM: A Near-Fatal Presentation With Difficult Management B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

P971 11:15 am-1:00 pm Not So Asymptomatic: A Large Pulmonary Arteriovenous Malformation B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

P331 11:15 am-1:00 pm Recurrent Hemoptysis Due To Diffuse Endobronchial Telangiectasia B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

Wednesday, May 22, 2019 P562 11:15 am-1:00 pm Solitary Pulmonary Nodule (SPN): Step Back Before A Needle D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

BENIGN METASTASIZING LEIOMYOMA


P472 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Case Of Not So "Benign" Metastasizing Leiomyomatosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P261 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Cancer Not Cancer: A Rare Case Of Metastatic Pulmonary Nodules D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P255 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Benign Metastasizing Leiomyoma: A Case Report D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P308 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm

A Woman With Bilateral Pulmonary Nodules: A Rare Case Of Benign Metastasizing Leiomyoma D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

BIRT-HOGG-DUBE SYNDROME


9:15 am-11:15 amOral Presentation 10:45 am-11:00 am

Canonical WNT Signaling Activity Is Decreased In Multiple Models Of Birt-Hogg-Dube C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD

P991 9:15 am-4:15 pm An Unsuspected Cause Of Spontaneous Pneumothorax: Birt-Hogg-Dube Syndrome C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD


P489 9:15 am-3:30 pm A Rare Form Of Cystic Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P488 9:15 am-3:30 pm A Pulmonologist's Conundrum: A Patient With Triple Threat Of Pulmonary Embolism, Cystic Lung Disease, And Pneumothorax D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P486 9:15 am-3:30 pm Severe Cystic Lung Disease And A Renal Mass In A 35-Year-Old Man: Diagnostic And Management Challenges D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

5

Rare Disease Term


ADULT

ADULT

Wednesday, May 22, 2019 P501 9:15 am-3:30 pm Birt-Hogg-Dubé Syndrome Diagnosed In A Patient Presenting With Dyspnea D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

BRONCHIOLITIS

Sunday, May 19, 2019 P1052 9:15 am-4:15 pm Forced Oscillation Technique In The Evaluation Of Biopsy-Confirmed

Constrictive Bronchiolitis In A Southwest Asia Deployed VeteranA49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD

Monday, May 20, 2019 317 9:15 am-11:15 am Murine Modeling Of Deployment-Related Chronic Bronchiolitis By

Conditional Depletion Of Airway Club Cells B28: HOW AIRWAYS MALFUNCTION: NEW CONCEPTS Ballroom A Four (Level 2), KBHCCD

P956 9:15 am-4:15 pm Who Group What, Where, When, Why And How B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

709 2:15 pm-4:15 pm Airway Epithelial Progenitor Cell Dysfunction After Flavoring-Induced Vapor Exposure

B107: EFFECTS OF E-CIGARETTES AND THEIR COMPONENTS ON RESPIRATORY DYSFUNCTION, INFLAMMATION, AND REPAIR Ballroom D Four (Level 3), KBHCCD

Tuesday, May 21, 2019 9:15 am-11:15 am Parametric Response Mapping Identifies Increased Functional Small Airways

Disease In Soldiers With Biopsy Evidence Of Chronic Bronchiolitis C15: OCCUPATIONAL EXPOSURES OF THE 21ST CENTURY Room D167/D174 (Level 1), KBHCCD

P1000 9:15 am-4:15 pm Follicular Bronchiolitis — A Diffuse Cystic Lung Disease Masquerading As Severe Obstructive Lung Disease C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD

Wednesday, May 22, 2019 113 9:15 am-11:15 am L-CSA, A Liposomal Formulation Of Cyclosporine A, Demonstrates Therapeutic

Potential For Bronchiolitis Obliterans Syndrome (BOS)D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND TRANSPLANT Room C140/C142 (Level 1), KBHCCD

P513 9:15 am-3:30 pm Idiopathic Obliterative Bronchiolitis Masquerading As Interstitial Lung Disease D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P516 9:15 am-3:30 pm A Case Of Bronchiolitis Obliterates Diagnosed By An Ultrathin Bronchoscopy After Bone Marrow Transplantation D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P544 9:15 am-3:30 pm A Rarity In The Airways D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

CASTLEMAN’S DISEASE


P1118 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Sarcomatoid Carcinoma Of The Lung: A Rare And Unfortunate Disease A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS

NOT ALWAYS WHAT YOU GET Area J (Hall F, Level 2), KBHCCD

6

Rare Disease Term


ADULT

ADULT

CTD-ILD


505 2:15 pm-4:15 pmPoster Viewing 2:15 pm-2:45 pmPoster Discussion 2:45 pm-4:15 pm

Plasma Biomarkers Of Survival In Patients With Interstitial Lung Disease A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD


Nailfold Capillaroscopy Findings In Ild Patients: Results From A Single Centre Investigation A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD

504 2:15 pm-4:15 pmPoster Viewing 2:15 pm -2:45 pmPoster Discussion 2:45 pm-4:15 pm

Nailfold Capillaroscopy In A Prospective Interstitial Lung Disease (ILD) Cohort: IPF, CTD-ILD And IPAF A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD



Epidemiology And Effect Of Therapy In Patients With Interstitial Pneumonia With Autoimmune Features (IPAF) B17: ADVANCES IN ILD THERAPY Room C155-C156 (Level 1), KBHCCD

P203 9:15 am-4:15 pmPoster Viewing 2:15 pm-2:45 pm

Prognostic Analysis Of Idiopathic Interstitial Pneumonias With Rheumatologic Features: A Prospective Multicenter Cohort Study (Pair Cohort Study) B46: IDIOPATHIC INTERSTITIAL PNEUMONIA: NATURAL HISTORY Area B (Hall F, Level 2), KBHCCD



Relapsing Polychondritis Patients With Tracheomalacia Have A Lower FEV1/FVC And FEF 25-75% As Well As A Previous Diagnosis Of Asthma C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Long-Term Evaluation Of Pulmonary Function Tests In Subgroups Of Patients With Interstitial Pneumonia With Autoimmune Features C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Autoimmune Serologies Predict Response To Treatment In Patients With Connective Tissue Related Interstitial Lung Disease (CTD-ILD) C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD


Effect Of Cotreatment With Corticosteroids In Connective Tissue Related Lung Disease (CTD-ILD) Patients On Mycophenolate Mofetil (MMF) C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD


Prognosis And Pulmonary Manifestations Of A Cohort Of Patients Positive To TH/TO Autoantibodies. C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD


9:15 am-11:15 amPoster Viewing 11:15 am-1:00 pmOral Presentation 10:45 am-11:00 am

Hospital Length Of Stay Following Lung Transplantation For Connective Tissue Disease-Associated Interstitial Lung Disease And Idiopathic Pulmonary Fibrosis

D13: TRANSPLANTATION Room C146 (Level 1), KBHCCD

7

Rare Disease Term


ADULT

ADULT


103 9:15 am-11:15 amPoster Viewing 11:15 am-1:00 pmPoster Discussion 10:00 am-11:15 am

Comparative Evaluation Of Radiographic And Autoimmune Serologic Features Between ANCA-Associated ILD And IPAF

D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND TRANSPLANT Room C140/C142 (Level 1), KBHCCD

CYSTIC LUNG DISEASE — OTHER



Unusual Case Of Diffuse Cystic Lung Disease Due To Metastatic Choriocarcinoma

A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS NOT ALWAYS WHAT YOU GET Area J (Hall F, Level 2), KBHCCD


A Brewing Case Of Malt Lymphoma: Primary Pulmonary Lymphoma Presenting As Cystic Lung Disease



P607 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Case Of Vanishing Lung Syndrome: A Rare Form Of Bullous Emphysema B64: COPD: MECHANISM AND TREATMENT Area D (Hall F, Level 2), KBHCCD



Follicular Bronchiolitis — A Diffuse Cystic Lung Disease Masquerading As Severe Obstructive Lung Disease C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD


P464 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Etiology Of Diffuse Cystic Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P474 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Cystic Lung: Manifestation Of Light Chain Deposition Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P485 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm An Uncommon Cause Of Cystic Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P495 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Holy Cysts! A Rare Pulmonary Manifestation Of Von Recklinghausen's Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P522 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Smoking-Related Diffuse Cystic Lung Disease D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

DERMATOMYOSITIS/ANTISYNTHETASE SYNDROME



Diverse Clinical Features Of Interstitial Lung Disease In Patients With The Anti-SSA-52 KD Myositis-Associated Autoantibody A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD

8

Rare Disease Term


ADULT

ADULT



Prognostic Factors Of Clinical Evolution In Patients With Antisynthetase Syndrome Treated With Methotrexate, Leflunomide & Prednisone A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


Prevalence And Diagnostic Implications Of Myositis-Specific Antibodies In Interstitial Lung Disease A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


Significance And Predictive Factors Of Recurrence In Anti-Aminoacyl-TRNA Synthetase Antibodies-Interstitial Lung Disease A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD



Clinical Characteristics Dermatomyositis/Polymyositis Associated Interstitial Lung Disease According To The Autoantibody C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Methotrexate Leflunomide In The Treatment Of Patients With Interstitial Lung Disease Positive To Antisynthetase Autoantibodies (Antisynthetase Syndrome) C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


The Change Of Ct Findings Of Treatment In Anti-MDA5 Autoantibodies Positive Dermatomyositis And RP-ILD C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Secondary Pulmonary Alveolar Proteinosis Presenting As Steroid Non-Responsive Interstitial Lung Disease In Anti-MDA5 Associated Amyopathic Dermatomyositis

C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND CLINICAL STUDIES Area G (Hall F, Level 2), KBHCCD


Prognostic Significance Of Macrophage-Mannose Receptor, CD206, In Anti-MDA5 Antibody-Positive Dermatomyositis-Associated Interstitial Lung Disease

C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD


104 9:15 am-11:15 amPoster Viewing 9:15 am-10:00 amPoster Discussion 10:00 am-11:15 am

Anti-TRNA Synthetase And Anti-PM/SCL Antibody Status Is Associated With Distinct Immunophenotypes Irrespective Of Clinical Classification


DIPNECH



A Rare Case Report: Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


30-Year-Old Female With Chronic Cough: A Presentation Of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH) D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

9

Rare Disease Term


ADULT

ADULT

DRUG INDUCED LUNG DISEASE

Sunday, May 19, 2019 P471 9:15 am-4:15 pm

Poster Viewing 11:15 am-1:00 pmIMATINIB-Induced Pneumonitis Associated With “Radiation-Recall” Pattern In A Patient With Chronic Myelogenous Leukemia And Prior Chemotherapy, Radiation Therapy, And Immunotherapy For Non-Small Cell Lung Cancer

A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P472 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Acute Drug-Induced Pneumonitis From Brentuximab Therapy D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE

REPORTS Area D (Hall F, Level 2), KBHCCD


A Case Of Eosinophilic Pneumonia Secondary To Ustekinumab In The Treatment Of Crohn's Disease A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Ruxolitinib Discontinuation Syndrome In A Patient With Myelofibrosis To Acute Myeloid Leukemia Transformation A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Unexplained Diffuse Alveolar Hemorrhage Associated With Recent Gingko Use A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P481 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Long Term Consequences Of A Rare Entity: Severe Contrast Aspiration D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


Onset Of ILD And Exacerbation Of Long Standing Myositis By Statin In Patient With Anti-Hmgcr Antibody A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Enasidenib Causing Differentiation Syndrome And Pulmonary Complications In A Patient With Acute Myeloid Leukemia A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Mammalian Target Of Rapamycin (MTOR) Inhibitor Induced Pulmonary Alveolar Proteinosis A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P498 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Dyspnea And Dry Eyes After Pembrolizumab D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P501 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Dress Syndrome Without Eosinophilia And Tuberculosis Treatment D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P505 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Two Cases Of Daptomycin-Induced Acute Eosinophilic Pneumonia A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

10

Rare Disease Term


ADULT

ADULT



Emerging Risk Profile Of Lung Cancer Immunotherapy: Unilateral Diffuse Alveolar Hemorrhage From Osimertinib A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P511 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Paclitaxel Induced Diffuse Interstitial Pneumonitis: A Case Report D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P515 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm ARDS: A Complication Of TALC Pleurodesis A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


P439 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Methotrexate-Induced Hypersensitivity Pneumonitis D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P440 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Amiodarone Induced Diffuse Alveolar Hemorrhage, A Rare Manifestation D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE



A Rare Cause Of Respiratory Failure: Daptomycin Induced Acute Eosinophilic Pneumonia A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P442 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Valproic Acid Associated Pleural Effusion D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P444 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Moxifloxacin Induced Hypersensitivity Pneumonitis D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P445 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Flavocoxid-Induced Pulmonary Toxicity A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Rapidly Progressingorganising Pneumoniain Association With Tocilizumab Treatment And Underlying Rheumatoid Arthritis A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P449 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Alectinib (ALK Inhibitor) Induced Interstitial Lung Disease D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


Organizing Pneumonia Secondary To High Dose Everolimus Therapy For Endometrial Carcinoma


P457 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Linezolid Induced Interstitial Lung Disease A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

11

Rare Disease Term


ADULT

ADULT


P594 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Bilateral Recurrent Chylothorax Following Treatment With Dasatinib D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P607 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Eosinophilic Pleural Effusion Due To Topical Minoxidil Use D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

EOSINOPHILC DISORDERS

Sunday, May 19, 2019 P475 9:15 am-4:15 pm A Case Of Eosinophilic Pneumonia Secondary To Ustekinumab In The

Treatment Of Crohn's Disease A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P476 9:15 am-4:15 pm Hypereosinophilic Syndrome With Acute Respiratory Failure Due To Severe Obstructive Airway Disease In A Patient Receiving Pembrolizumab A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P505 9:15 am-4:15 pm Two Cases Of Daptomycin-Induced Acute Eosinophilic Pneumonia A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P520 9:15 am-4:15 pm Idiopathic Chronic Eosinophilic Pneumonia With Bilateral Eosinophilic Effusions: A Unique Presentation Of A Rare Disease A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P565 9:15 am-4:15 pm Acute Idiopathic Eosinophilic Pneumonia. Not All Cases Are Alike, A Diagnostic Challenge A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P522 9:15 am-4:15 pm Management Of Chronic Eosinophilic Pneumonia With Mepolizumab A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P633 9:15 am-4:15 pm Concurrent Acute Eosinophilic Pneumonia And Mycobacterium Avium Complex In An Emphysematous Patient A57: NTM: CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P1035 9:15 am-4:15 pm Chronic Eosinophilic Pneumonia And Asthma Following Military Deployment A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD

P1036 9:15 am-4:15 pm When Mary Jane And Joe Camel Meet... Eosinophilic Sparks Are Born A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD

Monday, May 20, 2019 P9 9:15 am-4:15 pm Allergic Bronchopulmonary Aspergillosis (ABPA) Related Admissions In The

United States & It's Outcomes In Asthmatics B34: ALLERGIC DISEASE: CLINICAL STUDIES AND MECHANISMS Area A (Hall F, Level 2), KBHCCD

508 9:15 am-11:15 amPoster Discussion 10:00 am-11:15 am

Exhaled Breath Analysis For Prediction Of Responders To Mepolizumab In Patients With Severe Asthma B21: SEVERE ASTHMA: CLINICAL AND MECHANISTIC STUDIES Room D222-D224 (Level 2), KBHCCD

12

Rare Disease Term


ADULT

ADULT

Wednesday, May 22, 2019 P551 9:15 am-3:30 pm Casting Chronic Cough: A Case Of Plastic Bronchitis Due To Chronic

Eosinophilic Pneumonia In An Adult D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P1031 9:15 am-3:30 pm Atypical Presentation Of Allergic Bronchopulmonary Aspergillosis Mimicking Lung Cancer D31: ALLERGY AND ASTHMA CASE REPORTS Area H (Hall F, Level 2), KBHCCD

FAMILIAL/GENETIC ILD



Mucus Matters: Ferrets Demonstrate Restrictive Lung Physiology, Sustained Fibrosis, Mucociliary Decrement In Airways, And Aberrant Repair Following Bleomycin-Induced Pulmonary Fibrosis

A108: PATHOPHYSIOLOGY IN DIFFUSE PARENCHYMAL LUNG DISEASES Ballroom D Four (Level 3), KBHCCD


Negligible Telomere-Independent Effect Of Telomerase On Alveolar Epithelial Cells A61: EPITHELIAL BIOLOGY Area C (Hall F, Level 2), KBHCCD

Tuesday, May 21, 2019 9:15 am-11:15 am

Oral Presentation 9:45 am-10:00 amExpression Of Distinct Surfactant Protein-C (SFTPC) Mutation Classes Reveal Common Downstream Pathways From Alveolar Type 2 Cell Quality Control Dysfunction To Pulmonary Fibrosis

C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD


Cellular Consequences Of Uncharacterized Surfactant Protein-A2 (SFTPA2)-Gene Mutations Associated With Familial Idiopathic Pulmonary Fibrosis (IPF) And Lung Cancer

C58: MECHANISMS OF PULMONARY FIBROSIS Area C (Hall F, Level 2), KBHCCD

P434 9:15 am-4:15 pm Copa Syndrome: A Rare Occurrence Of Familial Ild With Rheumatoid Arthritis C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY LUNG DISEASES Area D (Hall F, Level 2), KBHCCD


Isolated Pulmonary Fibrosis: An Atypical Presentation Of Dyskeratosis Congenita


P957 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Fibrosis Due To A Novel Surfactant Protein Mutation C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND

CLINICAL STUDIES Area G (Hall F, Level 2), KBHCCD

P1051 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Genetic Studies On Brazilian Patients With Familial Interstitial Pneumonias C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD


The 5-Year Experience At A Pulmonary Genetics Center: Diverse Presentations, Rapid Growth, And Frequent Molecular Diagnosis C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD

13

Rare Disease Term


ADULT

ADULT



The Prevalence And Progression Of Early Interstitial Lung Disease In First-Degree Relatives Of Patients With Familial Interstitial Pneumonia

D103: IDIOPATHIC INTERSTITIAL PNEUMONIAS: NATURAL HISTORY AND PROGNOSIS Room C140/C142 (Level 1), KBHCCD


The Effects Of Tobacco Smoking Intensity And Cessation On Idiopathic Pulmonary Fibrosis Incidence And Progression

D103: IDIOPATHIC INTERSTITIAL PNEUMONIAS: NATURAL HISTORY AND PROGNOSIS Room C140/C142 (Level 1), KBHCCD

P432 9:15 am-3:30 pm Lung Transplantation In A Patient With Gaucher Disease Type 1: A Case Report And Review Of The Literature.


P469 9:15 am-3:30 pmRecurrent Pneumonia In Pregnancy Unveils Common Variable Immunodeficiency And Associated Granulomatous Lymphocytic Interstitial Lung Disease

D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

HEPATOPULMONARY SYNDROME



Effects Of Aerobic Training On Respiratory Mechanics And Lung Inflammation In Rats With Hepatopulmonary Syndrome

A59: PULMONARY REHABILITATION: MUSCLE FUNCTION AND STRENGTH Area C (Hall F, Level 2), KBHCCD


Effects Of Combined Exercise Training In Respiratory System Mechanical Properties And Inflammation In Rats With Hepatopulmonary Syndrome

A59: PULMONARY REHABILITATION: MUSCLE FUNCTION AND STRENGTH Area C (Hall F, Level 2), KBHCCD


The Role Of Placental Growth Factor As A Mediator Of Pulmonary Disease Via Human Alveolar Type 2 Pneumocyte Apoptosis A61: EPITHELIAL BIOLOGY Area C (Hall F, Level 2), KBHCCD


P334 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm An Uncommon Etiology Of Platypnea-Orthodeoxia Syndrome B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD

P343 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Case Of Hepatopulmonary Syndrome B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD


Successful Treatment Of Severe Hepatopulmonary Syndrome With Primary Embolotherapy Prior To Potential Liver Transplant B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

14

Rare Disease Term


ADULT

ADULT

HERMANSKY PUDLAK SYNDROME



Effective Anti-Fibrotic Therapy For Hermansky-Pudlak Syndrome Pulmonary Fibrosis In Pale Ear Mice Using A Hybrid Inhibitor Of Cannabinoid Receptor 1 (Cb<Sub>1</Sub>R) And Inducible Nitric Oxide Synthase (iNOS), MRI-1867

A29: EMERGING CONCEPTS IN LUNG FIBROSIS Ballroom D Four (Level 3), KBHCCD



The Differential Effects Of Hermansky-Pudlak Syndrome 1 And 2 On Lung Fibroblast Behavior

C59: GENETIC AND EPIGENETIC MECHANISMS IN PULMONARY FIBROSIS Area C (Hall F, Level 2), KBHCCD


Shortened Telomeres In Type II Alveolar Epithelial Cells In Hermansky-Pudlak Syndrome Pulmonary Fibrosis


P425 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pathomechanistic Role Of Autophagy In The Development Of Lung Fibrosis C64: PULMONARY FIBROSIS MODELS AND MECHANISTIC

INSIGHTS Area C (Hall F, Level 2), KBHCCD



Hermansky-Pudlak Syndrome Subtype 4 (HPS-4): A Novel Mutation In A 44 Years Old Italian Woman With Severe Pulmonary Fibrosis D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Ap-3-Dependent Mechanisms Regulate The Trafficking Of ATP8A1 To Lamellar Bodies In Alveolar Type 2 Cells

D107: MITOCHONDRIA AND ER STRESS IN HOMEOSTASIS AND REPAIR Ballroom D Three (Level 3), KBHCCD

HHT



Multiple Pulmonary Abscesses As A Late Complication Of Pulmonary Arteriovenous Malformation Embolization B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P858 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Hereditary Hemorrhagic Telangiectasia Associated High-Output Heart Failure B51: CRITICAL CARE CASE REPORTS: CARDIOVASCULAR

DISEASES IN THE ICU II Area F (Hall F, Level 2), KBHCCD


Screening For Pulmonary Arteriovenous Malformation (PAVM) In Hereditary Hemorrhagic Telagiectasia: Clinical Significance Of Pulmonary Micronodules And/Or Positive TTCE Without PAVM

B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD

HISTIOCYTIC DISORDERS



Association Between Clinicopathologic Characteristics And BRAFV600E Expression In Chinese Patients With Langerhans Cell Histiocytosis A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD

15

Rare Disease Term


ADULT

ADULT


P462 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Langerhans Cell Histiocytosis In Adults A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD

P1108 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Rosai-Dorfman Disease: An Unusual Cause Of A Solitary Pulmonary Mass A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS




Secondary Hemophagocytic Lymphohistiocytosis Due To Kikuchi Fujimoto Disease/Systemic Lupus Erythematosus Overlap B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD



Clinical Outcomes And Survival Following Lung Transplantation In Patients With Pulmonary Langerhans Cell Histiocytosis C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Epidemiology And Healthcare Utilization Of Spontaneous Pneumothorax And Diffuse Cystic Lung Diseases In The United States



P480 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Langerhans Cell Histiocytosis And Iga Nephropathy D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Non-Langerhans Histiocytosis: A Unique Presentation Of Erdheim-Chester And IGG4 Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


The Many Faces Of Interstitial Lung Disease: Transformation Of Non Specific Interstitial Pneumonia Into Pulmonary Langerhans Cell Histiocytosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P498 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm All That Wheezes Is Not Asthma D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P503 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Erdheim-Chester Disease Presenting With Spontaneous Pneumothorax D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

HYPERSENSITIVITY PNEUMONITIS


707 9:15 am-11:15 am Poster Viewing 9:15 am-10:00 amPoster Discussion 10:00 am-11:15 am

Myeloid-Derived Suppressor Cells Orchestrate Immunosuppressive Networks In Idiopathic Pulmonary Fibrosis A29: EMERGING CONCEPTS IN LUNG FIBROSIS Ballroom D Four (Level 3), KBHCCD

P201 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Squawks In Interstitial Lung Diseases A38: IDIOPATHIC INTERSTITIAL PNEUMONIA: DIAGNOSIS AND

NATURAL HISTORY Area B (Hall F, Level 2), KBHCCD

16

Rare Disease Term


ADULT

ADULT



Rituximab For Stabilization Of Fibrotic Hypersensitivity Pneumonitis In A Patient With Continued Antigen Exposure A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Chronic Hypersensitivity Pneumonitis (CHP), An ILD With Distinct Molecular Signatures A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD

P1033 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Hypersensitivity Pneumonitis: A Clinical Case A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH

INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD



Development Of A Patient Centered Thematic Framework For Experiences Living With Chronic Hypersensitivity Pneumonitis; A Qualitative Study B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD

P149 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Transbronchial Biopsy In Chronic Hypersensitivity Pneumonitis B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD


Anti-Fibrotic Therapy For Chronic Hypersensitivity Pneumonitis: Don’t Forget The Antigen B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD


Causes Of Hypersensitivity Pneumonitis: Literature Review And Development Of A Knowledge Translation Tool B39: GRANULOMATOUS ILDs Area B (Hall F, Level 2), KBHCCD


Diagnostic Challenges And Management Considerations Of Immune-Related Hypersensitivity Pneumonitis Associated With Immune Checkpoint Inhibitors B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD



The Value Of High Resolution Computed Tomography And Surgical Lung Biopsy In Predicting Outcome For Patients With Fibrotic Hypersensitivity Pneumonia



Bronchoscopic Lung Biopsy For Diffuse Parenchymal Lung Disease: Comparison Of Forceps With Cryobiopsy C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD


Usefulness Of New Criteria For Chronic Hypersensitivity Pneumonitis Established By Delphi Method C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD

17

Rare Disease Term


ADULT

ADULT



Identification Of Indoor Fungal Antigens In Assessment Of Hypersensitivity Pneumonitis — An Alternate Approach C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD


Standard Panels, Environmental Samples, And Hypersensitivity Pneumonitis - Identification Of The Elusive ‘Causal Antigen’ C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD


Antinuclear Antibodies In Patients With Hypersensitivity Pneumonitis: Insights On Clinical Relevance From A German Double-Cohort Investigation. C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD


Custom Made Serological Method To Assess Relevant Source Of Exposure In Patients With Extrinsic Allergic Alveolitis C44: ASTHMA EPIDEMIOLOGY Area D (Hall F, Level 2), KBHCCD



Rare Protein-Altering Telomere-Related Gene Variants In Patients With Chronic Hypersensitivity Pneumonitis: An Observational Cohort Study D12: ILD: DIAGNOSIS AND PROGNOSIS Room C155-C156 (Level 1), KBHCCD

P23 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Red Tide Pneumonitis D47: CRITICAL CARE CASE REPORTS: INFECTION AND SEPSIS I Area A (Hall F, Level 2), KBHCCD


Spontaneous Pneumomediastinum In A Patient With Chronic Fibrotic Hypersensitivity Pneumonitis D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P546 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Ca 15.3 As A Marker Of Chronic Hypersensitivity Pneumonitis D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P1034 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Bulky Nodules: An Atypical Presentation Of Hypersensitivity Pneumonitis D31: ALLERGY AND ASTHMA CASE REPORTS Area H (Hall F, Level 2), KBHCCD

IDIOPATHIC PULMONARY HEMOSIDEROSIS


P473 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Gluten Intolerance Of The Lung D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


A Curious Cause Of Iron Deficiency Anemia: Idiopathic Pulmonary Hemosiderosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

18

Rare Disease Term


ADULT

ADULT

IGG4 RELATED DISEASE



Thoracic Paravertebral Lesions In Patients With IGG4-Related Respiratory Disease A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD

Monday, May 20, 2019 P244 9:15 am-4:15 pm

Poster Viewing 11:15 am-1:00 pmAcute Respiratory Distress Syndrome (ARDS) Complicating Pulmonary Nodular Lymphocytic Hyperplasia (PNLH) Associated With Immunoglobulin G4 Related Disorder (IGG4-Rd)

B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD


P438 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary IGG4 Disease — The New Masquerader? C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY

LUNG DISEASES Area D (Hall F, Level 2), KBHCCD

P451 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Airway And Bone Marrow Involvement In A Patient With IGG4-Related Disease C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY


P470 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Delayed Presentation Of IGG4 Related Lung Disease C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P958 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm IGG4 Related Disease: A Possible Cause Of Lymphoid Interstitial Pneumonia C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND




Bilateral Pulmonary Nodules Secondary To IGG4-Related Respiratory Disease: An Unusual Mimicker Of Malignancy D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Non-Langerhans Histiocytosis: A Unique Presentation Of Erdheim-Chester And IGG4 Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P499 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Recurrent Pleuritis: A Pulmonary Manifestation Of IGG4 Related Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

ILD — OTHERS


P545 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Granulomatous And Lymphocytic Ild (Glild): Revelation In Ild World A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Diffuse Large B-Cell Lymphoma Presenting As Progressive Interstitial Lung Disease


19

Rare Disease Term


ADULT

ADULT



Nailfold Capillaroscopy In A Prospective Interstitial Lung Disease (ILD) Cohort: IPF, CTD-ILD And IPAF A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD



Clinical Features Of Pathologically Proven Acute Fibrinous And Organizing Pneumonia B46: IDIOPATHIC INTERSTITIAL PNEUMONIA: NATURAL HISTORY Area B (Hall F, Level 2), KBHCCD


Physical Frailty In Fibrotic Lung Disease And Response To Pulmonary Rehabilitation B60: PULMONARY REHABILITATION: GENERAL Area B (Hall F, Level 2), KBHCCD


A Pilot Randomised Controlled Trial Of Ambulatory Oxygen Versus Air Via Portable Concentrator In Fibrotic Interstitial Lung Disease B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD



Diagnostic Delays In Interstitial Lung Diseases (ILDS) C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD


Single-Cell Transcriptomic Analysis Of Type 2 Alveolar Epithelial Cell Differentiation From Induced Pluripotent Stem Cells: An Emerging Tool To Model Interstitial Lung Diseases

C28: PATHWAYS OF LUNG MORPHOGENESIS Ballroom D Three (Level 3), KBHCCD


Melanocyte Stimulating Hormone Has Anti-Inflammatory Properties In Granuloma Via Marco And P-CREB C31: TRANSLATIONAL STUDIES IN SARCOIDOSIS Area C (Hall F, Level 2), KBHCCD


Pulmonary Lymphangiectasia: A Novel Histopathologic Finding In Coatomer Subunit Alpha (COPA) Syndrome

C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY LUNG DISEASES Area D (Hall F, Level 2), KBHCCD

P434 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Copa Syndrome: A Rare Occurrence Of Familial ILD With Rheumatoid Arthritis C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY


P456 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Rapidly Evolving Pulmonary Granulomas: A NOD2 Home Genetic Testing C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY



Possible Value Of Antifibrotic Drugs In Patients With Progressive Fibrosing Non-IPF Interstitial Lung Diseases C39: IDIOPATHIC INTERSTITIAL PNEUMONIA: THERAPY Area H (Hall F, Level 2), KBHCCD

114 2:15 pm-4:15 pmPoster Viewing 11:15 am-1:00 pm Recurrent Acute Exacerbations Of Fibrotic Interstitial Lung Diseases C101: NON-IDIOPATHIC INTERSTITIAL PNEUMONIA NATURAL

HISTORY AND PROGNOSIS AND ILD THERAPY Room C140/C142 (Level 1), KBHCCD

20

Rare Disease Term


ADULT

ADULT



Lung Allocation Score Should Be Implemented In China D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND TRANSPLANT Room C140/C142 (Level 1), KBHCCD


Single Cell Analysis Of Pulmonary Fibrosis Phenotypes D29: LUNG MULTI-OMICS TO MECHANISM Room D222-D224 (Level 2), KBHCCD

P459 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Case Of Interstitial Fibrosis Five Years After Bleomycin Exposure D38: LUNG TRANSPLANTATION AND DRUG RELATED CASE


P471 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Natural Course Of Pulmonary Hyalinizing Granuloma In A Decade D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P511 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm To Treat Or Not To Treat: The Dip Question D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P512 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Fibrosis And Embolism Secondary To Silicon Implant Leak D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


An Alternative Approach Of Diagnosing Diffuse Pulmonary Meningotheliomatosis (DPMS) With Transbronchial Cryobiopsy D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

LAM



Menstrual Cycle-Related Symptom Variability In Patients With Lymphangioleiomyomatosis A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Single Center Experience Of Lung Transplantation For Lymphangioleiomyomatosis A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Lymphangioleiomyomatosis (LAM) Nodules Attract And Activate Alveolar Type II Cells A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Exosomes Released From Lymphangioleiomyomatosis-Derived Smooth Muscle-Like Cells Mediate Endothelial Cell Apoptosis And Vascular Network Disruption

A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Mast Cell Recruitment In Lymphangiomatosis And Lung Cystic Destruction; Opportunities For Drug Repurposing A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD

21

Rare Disease Term


ADULT

ADULT



Identification Of Clinically Relevant Immunohistochemical Sub-Groups In The UK National Cohort Of Lymphangioleiomyomatosis (LAM). A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD

P371 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Role Of Kiss1 Signaling In Pulmonary Lymphangioleiomyomatosis A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD


Correlative Imaging Study Of Lymphangioleiomyomatosis Tissue Sample By X-Ray Micro Tomography And Histology A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD


Detailed Imaging Of Lung Cysts In Lam And Bhd Patients By A High-Resolution Targeted CT RE-SCAN A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD


A Phase Ii Clinical Trial Of The Safety Of Simvastatin In Patients With Pulmonary Lymphangioleiomyomatosis And With Tuberous Sclerosis Complex A66: LYMPHANGIOLEIOMYOMATOSIS (LAM) Area C (Hall F, Level 2), KBHCCD


Relationship Between Menopause And Development Of Spontaneous Pneumothorax In Females With Lymphangioleiomyomatosis A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Proteomic Profiling Of Serum Exosomes To Identify Novel Biomarkers For Lymphangioleiomyomatosis A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Delineating Novel Mtor-Independent Signaling Pathways For Lymphangioleiomyomatosis And Tuberous Sclerosis Therapy A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD

P466 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Targeting Akt As A Therapeutic Intervention In Treatment Of Lam A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Dysregulation Of Sphingolipid Metabolism In Pulmonary Lymphangioleiomyomatosis (LAM) A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD



Effects Of Yoga On Functional Capacity And Quality Of Life In The Participants With Lymphangioleiomyomatosis: A Pilot Study B60: PULMONARY REHABILITATION: GENERAL Area B (Hall F, Level 2), KBHCCD



Epidemiology And Healthcare Utilization Of Spontaneous Pneumothorax And Diffuse Cystic Lung Diseases In The United States



Targeted High-Resolution CT RE-SCAN In Patients With Lymphangioleiomyomatosis Lead To Higher Cyst Score Accuracy


22

Rare Disease Term


ADULT

ADULT



Lung Transplantation For Lymphangioleiomyomatosis: A Review Of The United Network For Organ Sharing Database


9:15 am-11:15 amOral Presentation 10:15 am-10:30 am NK Cell Activation Is Increased In Lymphangioleiomyomatosis C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD


Disruptive Effect Of LAM-Derived Smooth Muscle Cells On Human Lung Progenitors Is Dependent On Expression Of Translationally Controlled Tumour Protein

C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD


Identification Of Clinical Endotypes In Lymphangioleiomyomatosis To Improve Personalised Care C22: ILD: DIAGNOSIS Room C140/C142 (Level 1), KBHCCD


Prevalence And Clinical Characteristics Of Lymphangioleiomyomatosis In 97 Patients C35: HEALTH SERVICES RESEARCH IN COUGH, CF, AND ILD Area H (Hall F, Level 2), KBHCCD



A Case Of Lymphangioleiomyomatosis With Normal Vascular Endothelial Growth Factors D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Co-Existant Sarcoidosis And Lymphangioleiomyomatosis In A Patient With Cystic Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


‘Finding Pneumo’; A Series Of Unfortunate Events Leading To A Very Rare Diagnosis Of Lymphangioleiomyomatosis In A Male D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P475 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Lymphangioleiomyomatosis —A Stitch In Time, Saves Nine D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Sirolimusimproves Lymphangioleiomyomatosis And Pneumothoraxin A Patient With Tuberous Sclerosis Carrying A Novel TSC2 Mutation D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P497 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Case Of Tuberous Sclerosis Associated Lymphangioleimyomatosis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Tuberous Sclerosis With Lymphangioleiomyomatosis (LAM) Treated With Sirolimus: A Case Report D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Lymphangioleiomyomatosis In Patient With Segmental And Focal Glomerulosclerosis (SFGS) Colapsant — Case Report D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

23

Rare Disease Term


ADULT

ADULT

MOUNIER-KUHN SYNDROME



Mounier- Kuhn Syndrome: A Rare Cause Of Recurrent Respiratory Tract Infection

A48: CRITICAL CARE CASE REPORTS: CAUSES AND COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Area G (Hall F, Level 2), KBHCCD


P954 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Case Of Mounier-Kuhn Syndrome C65: DIFFUSE PARENCHYMAL LUNG DISEASES: BASIC AND



P633 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm More Than Just Chronic Obstructive Pulmonary Disease D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Case Of Mounier-Kuhn Syndrome: A Rare Disease Presenting With Recurrent Pneumonia And Bronchiectasis D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P644 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Tracheobronchomegaly A Case Of Mounier Kuhn’s Syndrome D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

MUCSCULAR DYSTROPHY



Identifying Potential Predictive Factors Of Sleep Quality In Duchenne Muscular Dystrophy

B65: SRN: DIAGNOSIS AND MONITORING OF SLEEP AND SLEEP DISORDERS Area K (Hall F, Level 2), KBHCCD



Bone Marrow-Derived Macrophages Of Duchenne Muscular Dystrophy (MDX) Mice Are Differentially “Educated” Based On Muscle Disease Stage

C109: RESPIRATORY MUSCLE DYSFUNCTION: MECHANISM AND ASSESSMENT Ballroom D Four (Level 3), KBHCCD

NEUROFIBROMATOSIS

Wednesday, May 22, 2019 P467 D5 9:15 am-3:30 pm Intrathoracic Ganglioneuromas In A Patient With Neurofibromatosis Type I D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P959 9:15 am-3:30 pm Pulmonary Arterial Hypertension: A Rare, Yet Life-Threatening Complication Of Neurofibromatosis Type 1 D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD

NON-CF BRONCHIECTASIS



Clinical Phenotypes Among Patients With Bronchiectasis C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO TREATMENT Ballroom A Four (Level 2), KBHCCD

24

Rare Disease Term


ADULT

ADULT



Airway Clearance In Non-Cystic Fibrosis Bronchiectasis: Analysis From The United States Bronchiectasis Research Registry

C105: BRONCHIECTASIS: FROM CLINICAL PHENOTYPES TO TREATMENT Ballroom A Four (Level 2), KBHCCD


Pseudomonas Aeruginosa Is Associated With Greater Frequency Of Exacerbations Among Patients With Non-Cystic Fibrosis Bronchiectasis In The United States



Effects Of Complex Heterozygosity Of Cftr And Ciliary Genes In Non-Cf Bronchiectasis



Inhaled Ciprofloxacin (ARD-3150) In Patients With Non-Cystic Fibrosis Bronchiectasis And Frequent Pulmonary Exacerbations: A Pooled Analysis From Orbit-3 And Orbit-4



Pseudomonas Aeruginosa Associated With Severity Of Non-Cystic Fibrosis Bronchiectasis Measured By The Modified Bronchiectasis Severity Score (BSI) And The Faced: The US Bronchiectasis And NTM Research Registry (BRR) Study



P571 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Selective Iga Deficiency And Bronchiectasis D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD


A Triple Threat: Acute Pulmonary Emboli, Pneumococcal Pneumonia And Congenital Bronchiectasis With Auto-Pneumonectomy And Compensatory Hyper-Lobar Expansion

D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P646 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Kartagener Syndrome In Identical Male Twins D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P645 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Parasitic Infection Leading To Bronchiectasis D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

OCCUPATIONAL/EXPOSURE RELATED LUNG DISORDERS


P1051 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Titanium Lung In A Solider With Iraq/Afghanistan War-Lung Injury (IAW-LI) A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH


25

Rare Disease Term


ADULT

ADULT



Airway Disease In Biomass Smoke-Associated Ild: Not Just Copd A104: WILDFIRE, BIOMASS, AND WORLD TRADE CENTER EXPOSURES

Trinity Ballroom 5-7 (Level 3), Omni Dallas Downtown


Sarcoid-Like Granulomatous Disease: Pathologic Case Series In World Trade Center (WTC) Dust Exposed Rescue And Recovery Workers

A104: WILDFIRE, BIOMASS, AND WORLD TRADE CENTER EXPOSURES



Forced Oscillation Technique In The Evaluation Of Biopsy-Confirmed Constrictive Bronchiolitis In A Southwest Asia Deployed Veteran

A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD

P1045 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Occupational Polycaprolactone Inhalation Induced Acute Lung Injury A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH



Titanium Is Abundant In Fibrotic Lungs Of Two Soldiers Post-Deployment To Iraq And Afghanistan But Is Not Seen In Lungs Of Five Patients With Idiopathic Pulmonary Fibrosis

A52: SARCOIDOSIS AND EXPOSURE RELATED INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


Healthcare Utilization Among Medicare Beneficiaries With Coal Worker’s Pneumoconiosis In The Us

A52: SARCOIDOSIS AND EXPOSURE RELATED INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD

P477 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Talc Granulomatosis Masquerading As A Tree In Bud Phenomenon A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Cavitary Lung Mass From Granulomatous Talc Disease Precipitated By Radiation Therapy A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P967 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Fatal Case Of Foreign-Body Granulomatous Pulmonary Emboli B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


1006 9:15 am-11:15 amPoster Viewing 11:15 am-1:00 pm

Epigenetic Signatures Of Sensitization And Disease In Beryllium-Exposed Individuals

B25: OCCUPATIONAL EXPOSURES INCLUDING DEPLOYMENT RELATED, MINING, AND AGRICULTURE



Pneumoconiosis Mortality: Progress Towards Healthy People 2020 Goal B25: OCCUPATIONAL EXPOSURES INCLUDING DEPLOYMENT RELATED, MINING, AND AGRICULTURE



P525 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Long Term Minimally Progressive Interstitial Fibrosis In A Dental Technician D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

26

Rare Disease Term


ADULT

ADULT



Recombinant Neuroglobin Reverses The Molecular Mitochondrial Effects Of Carbon Monoxide Poisoning Through Carbon Monoxide Scavenging

D26: HEALTH EFFECTS ASSOCIATED WITH INDOOR AND OUTDOOR AIR POLLUTION Arena (Level 2), KBHCCD


"But I Never Smoked!!!" - A Case Of Respiratory Bronchiolitis Interstitial Lung Disease In A Non-Smoker D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

PCH AND PVOD



Rapid Diagnosis Of Pulmonary Veno-Occlusive Disease With Bedside Ultrasonography A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD



Pulmonary Veno-Occlusive Disease In Apatient With C282y Homozygous Mutation B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


A Case Of Pulmonary Veno-Occulssive Disease With Variant In Eif2ak4 C.892Dela B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


Pulmonary Veno-Occlusive Disease In Elderly Patients With Hypoxemia Out Of Proportion To Underlying Pulmonary Or Cardiovascular Disease: An Under-Recognized Entity?

B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD

Tuesday, May 21, 2019 P1137 9:15 am-4:15 pm

Poster Viewing 11:15 am-1:00 pmMitomycin C Induces Pulmonary Vessel Endothelial-To-Mesenchymal Transition And Pulmonary Veno-Occlusive Disease Via Smad3-Dependent Pathway In Rats

C50: THE PERFECT DRUG: EXPERIMENTAL TREATMENTS OF PAH Area J (Hall F, Level 2), KBHCCD


P971 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm The Never Ending Battle Between The Heart And The Lung D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD

P967 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Looks And Smells Like PAH...The Great Mimicker “PVOD” D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD

PLASTIC BRONCHITIS


P1020 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Plastics In The ICU A48: CRITICAL CARE CASE REPORTS: CAUSES AND

COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Area G (Hall F, Level 2), KBHCCD



Lymphatic Plastic Bronchitis With Chyloptysis Secondary To Thoracic Duct Stenosis C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD

27

Rare Disease Term


ADULT

ADULT



Casting Chronic Cough: A Case Of Plastic Bronchitis Due To Chronic Eosinophilic Pneumonia In An Adult D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

PPFE



Clinical Courses Of Asymptomatic Patients With Mild Idiopathic Pleuroparenchymal Fibroelastosis B46: IDIOPATHIC INTERSTITIAL PNEUMONIA: NATURAL HISTORY Area B (Hall F, Level 2), KBHCCD


Treatment With Antifibrotic Agents In Pleuroparenchymal Fibroelastosis With Usual Interstitial Pneumonia B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD



A Case Of The Usual/Unusual: Pleuroparenchymal Fibroelastosis Misdiagnosed As Sarcoidosis D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P533 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Case Study On Pleuroparenchymal Fibroelastosis — Is It Really An Enigma? D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Pleuroparenchymal Fibroelastosis Progressing To Unilateral Vocal Cord Paralysis D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Secondary Spontaneous Pneumothorax As A Complication Of Pleuroparenchymal Fibroelastosis: A Case Report D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Coexisting Together: Pleuroparenchymal Fibroelastosis With Usual Interstitial Pneumonia D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

PRIMARY CILIARY DYSKINESIA



AC6 Regulates Microtubule-Depolymerizing Kinesin KIF19a For Ciliary Length Control In Mammals A62: MUCUS, MUCINS, MUCOCILIARY UNIT IN LUNG DISEASE Area C (Hall F, Level 2), KBHCCD



Airways Mucus Pathogenesis In Patients With Non-Cystic Fibrosis Bronchiectasis And Primary Ciliary Dyskinesia


9:15 am-11:15 amOral Presentation 10:00 am-10:15 am NEK10 Loss Of Function Causes A Novel Human Motile Ciliopathy C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD

28

Rare Disease Term


ADULT

ADULT



Quantitative High Speed Video Profiling Discriminates Between Variants Of Primary Ciliary Dyskinesia D18: BEST OF NOVEL TECHNOLOGIES AND METHODOLOGIES Room D167/D174 (Level 1), KBHCCD


Beyond Young’s Syndrome: Diagnosis, Management, And Prognosis Of Primary Ciliary Dyskinesia. D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P643 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Journey Of A Patient With Kartagener’s Syndrome D43: COPD, CF, AND BRONCHIECTASIS CASE REPORTS Area D (Hall F, Level 2), KBHCCD

PULMONARY ALVEOLAR PROTEINOSIS



Prognostic Impacts Of Comorbidities In Pulmonary Alveolar Proteinosis: A Nationwide Surveillance In Japan A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD

P456 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm An Approach To Precision Medicine For Pulmonary Alveolar Proteinosis A36: RARE LUNG DISEASES FROM BENCH TO BEDSIDE Area D (Hall F, Level 2), KBHCCD


Mammalian Target Of Rapamycin (MTOR) Inhibitor Induced Pulmonary Alveolar Proteinosis A39: DRUG RELATED CASE REPORTS Area D (Hall F, Level 2), KBHCCD


A Case Of Severe Acute Respiratory Distress Syndrome With Underlying Pulmonary Alveolar Proteinosis That Could Not Be Saved With Extracorporeal Membrane Oxygenation

A47: CRITICAL CARE CASE REPORTS: MECHANICAL VENTILATION FROM NIV TO ECMO Area G (Hall F, Level 2), KBHCCD


Pulmonary Alveolar Proteinosis And P-ANCA Glomerulonephritis Post Silica Exposure

A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH INHALATIONAL EXPOSURES Area H (Hall F, Level 2), KBHCCD



Us National Pulmonary Alveolar Proteinosis Registry: Update On Differential Diagnosis, Clinical Manifestations, And Current Therapy B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD


A Case Of Autoimmune Pulmonary Alveolar Proteinosis With Sjögren’s Syndrome B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD


Pulmonary Alveolar Proteinosis: A Rare Case Of Autoimmune Disruption Of Gm-Csf Superimposed With Secondary Inhalation Exposure B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD

29

Rare Disease Term


ADULT

ADULT


P242 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm The Surfactant Of The Matter: A Case Of Severe Pulmonary Alveolar Proteinosis B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD


Effect Of Pioglitazone Therapy On Alveolar Macrophage Size In A Patient With Refractory Autoimmune Pulmonary Alveolar Proteinosis B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD


Primary Pulmonary Alveolar Proteinosis In A Patient With Chronic Lymphoblastic Leukemia B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P338 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Alveolar Proteinosis (PAP) B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD


P436 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Severe Pulmonary Alveolar Proteinosis In A Patient With GATA2 Deficiency C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY



Effect Of Whole Lung Lavage (Wll) On Exhaled Nitric Oxide Fraction (FENO) In Patients With Autoimmune Pulmonary Alveolar Proteinosis (APAP) C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Clinical Observation: 5 Cases Of Wen San Ding Transdermal External Treatment For Idiopathic Pulmonary Alveolar Proteinosis C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Lipid Accumulation Leads To Inhibition Of M1 Response In Alveolar Macrophages



Secondary Pulmonary Alveolar Proteinosis Presenting As Steroid Non-Responsive Interstitial Lung Disease In Anti-Mda5 Associated Amyopathic Dermatomyositis


P983 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Too Much Protein! C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD

Wednesday, May 22, 2019 P465 9:15 am-3:30 pm

Poster Viewing 11:15 am-1:00 pmLong-Term Follow-Up Of A Patient With GM-CSF Antibody-Negative Pulmonary Alveolar Proteinosis Following Exposure To Dust After The Great East Japan Earthquake

D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Dramatic Response Of Rituximab In Severe Autoimmune Pulmonary Alveolar Proteinosis: A Case Report D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

30

Rare Disease Term


ADULT

ADULT


P478 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Alveolar Proteinosis—A Washed Up Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

PULMONARY ARTERY ANEURYSMS



Death By Behcet: A Case Ofpulmonary Artery Aneurysm Secondary To Active Behcet's Vasculitis A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD



Thrombosed Pulmonary Artery Aneurysm In A Patient With Underlying Eosinophilic Granulomatosis With Polyangiitis B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


An Unusual Case Of Pulmonary Artery Aneurysms With Mural Thrombus Formation B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


Outcomes Of Pulmonary Artery Aneurysms In Patients With Pulmonary Hypertension. A Single Center Experience B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD


P21 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Rasmussen's Aneurysm: A Rare And Potentially Fatal Cause Of Hemoptysis C53: TUBERCULOSIS CASE REPORTS Area A (Hall F, Level 2), KBHCCD


P264 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Squamous Cell Carcinoma Causing Rasmussen Aneurysm D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

PULMONARY OSSIFICATION, CALCIFICATIONS, AND MICROLITHIASIS


P1043 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Fumes On A Plane! A Case Of DPO A49: CASE REPORTS IN LUNG DISEASE ASSOCIATED WITH




When Lungs Become Bone: A Rare Case Of Idiopathic Dendriform Pulmonary Ossification B42: DYSPNEA CASE REPORTS Area C (Hall F, Level 2), KBHCCD


9:15 am-11:15 amOral Presentation 11:00 am-11:15 am Osteogenesis And Osteolysis In Pulmonary Alveolar Microlithiasis C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD


P462 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Calcified Curse: A Case Of Pulmonary Alveolar Microlithiasis D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Concrete Heavy Lungs Due To Calcium Stones: Pulmonary Alveolar Microlithiasis: A Rare Lung Disease D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

31

Rare Disease Term


ADULT

ADULT


P487 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Dishing Out Pulmonary Calcifications D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P492 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Should I Get An Ortho Consult?: A Case Of Pulmonary Ossification D39: RARE DPLD CASE REPORTS Area D (Hall F, Level 2), KBHCCD


An Uncommon Presentation Of An Uncommon Disorder: Dendriform Pulmonary Ossification D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD


Dendriform Pulmonary Ossification Complicated By Recurrent Spontaneous Pneumothorax D40: NON-INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD

RARE AIRWAY DISORDERS



The Establishment Of Two Animal Models Of Benign Airway Stenosis And The Therapeutic Effect Of Mitomycin C On Airway Stenosis

A68: NEW TECHNIQUES, METHODOLOGIES, AND MATHEMATICAL MODELING Area C (Hall F, Level 2), KBHCCD

P1114 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Mimicking Lung Cancer: Pulmonary Sclerosing Pneumocytoma A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS


P1147 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Rare Occurrence Of Endobronchial Granular Cell Tumor A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD


Endobronchial Choriocarcinoma Presenting With Hemoptysis Six Weeks After A Normal Vaginal Delivery: A Bronchoscopic Diagnostic Challenge A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD

P1139 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Endobronchial Chondroma As A Rare Cause Of Hemoptysis A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD

P1140 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Kaposi Sarcoma: Bronchoscopy And Imaging Findings A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD


Tracheal Adenoid Cystic Carcinoma Presenting With Recurrent Wheeze And A "Normal" Chest X-Ray A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD



Excessive Dynamic Airway Collapse In A Young Woman With Hypermobility-Type Ehlers-Danlos Syndrome B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

32

Rare Disease Term


ADULT

ADULT

Monday, May 20, 2019 P314 9:15 am-4:15 pm

Poster Viewing 11:15 am-1:00 pmIncidentally Discovered "Rock Garden"- Tracheobronchoplastica Osteochondropathica With Associated Left Sided Breast Adenocarcinoma And Severe Esophageal Strictures: A Rare Case Report

B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


Management Of A Case Of Tracheobronchopathia Osteochondroplastica Causing Airway Obstruction B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P57 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Diagnostic Challenges Of Pulmonary Kaposi Sarcoma In AIDS Patients B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT

DILEMMAS Area A (Hall F, Level 2), KBHCCD


A Population-Based Description Of Incidence And Familial Clustering Of Pulmonary Carcinoid Tumors

B69: THORACIC ONCOLOGY: OPTIMIZING DIAGNOSIS AND MANAGEMENT Area A (Hall F, Level 2), KBHCCD


P465 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm My Oh! A Case Of Endobronchial Leiomyoma C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


You Have Mucous Membrane Pemphigoid, Causing Subglottic Stenosis, And You Lived To Tell About It? C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P482 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Rare Case Of Endobronchial Schwannoma C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P500 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Benign Bump: A Rare Case Of Endobronchial Chondroma C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P502 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Endobronchial Leiomyoma: A Rare Form Of Bronchial Tumor C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD



Not Your Usual Chronic Cough — A Case Of Lymphomatoid Granulomatosis With Tracheal Obstruction D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

RARE CONGENTIAL ANOMALIES


P1006 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm The Unexpected Tracheal Bronchus A48: CRITICAL CARE CASE REPORTS: CAUSES AND

COMPLICATIONS OF ACUTE RESPIRATORY FAILURE Area G (Hall F, Level 2), KBHCCD

P827 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Scimitar Syndrome: A Rare Cause Of Cardiomyopathy In Adults. A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD

33

Rare Disease Term


ADULT

ADULT



A Case Of Pulmonary Hypertension And Undiagnosed Atrioventricular Canal In An Adult Patient A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD

P847 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Right Ventricular Diverticulum In Scimitar Syndrome A54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE I Area F (Hall F, Level 2), KBHCCD



Excessive Dynamic Airway Collapse In A Young Woman With Hypermobility-Type Ehlers-Danlos Syndrome B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


Persistent Left Superior Vena Cava With Partial Anomalous Pulmonary Venous Return In A Patient With Atrial Fibrillation: A Case Report

B51: CRITICAL CARE CASE REPORTS: CARDIOVASCULAR DISEASES IN THE ICU II Area F (Hall F, Level 2), KBHCCD

P960 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Pathology In Abernethy Malformation B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


Mistaken Identity: A Case Of High-Output Pulmonary Hypertension Due To Partial Anomalous Pulmonary Venous Drainage Disguised By An Arterio-Venous Fistula

B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

P968 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Different Kind Of Vascular Shunt In A Hemodialysis Patient With Chest Pain B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

P970 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm An Undiagnosed Left Persistent Superior Vena Cava: The Role Of Pocus B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


Always Consider The Birthmark: A Rare Case Of A Right Middle Intralobar Bronchopulmonary Sequestration In An Adult B59: BACTERIAL INFECTION CASE REPORTS Area H (Hall F, Level 2), KBHCCD



An Incidental Finding Of A Tracheal Bronchus In A Rheumatoid Arthritis Patient: Case Report C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P989 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Case Of Asymptomatic Swyer-James-Macleod Syndrome C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD

P990 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Stay Calm And Just Breathe: A Case Of Swyer-James-Mcleod Syndrome C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD


P951 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Congenital Pulmonary Malformation In An Adult Patient: Case Report D55: CASE REPORTS IN PULMONARY VASCULAR MEDICINE III Area G (Hall F, Level 2), KBHCCD

34

Rare Disease Term


ADULT

ADULT


P243 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Case Of Bronchopulmonary Sequestration Causing Recurrent Pneumonia D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

RARE NON-MALIGNANT PLEURAL DISORDERS


P417 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Gastronomic Pleurisy: A Case Of Pancreatic Pleural Fistula B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


P573 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Primary Malignant Myelomatous Pleural Effusion: A Rare Entity D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P580 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Case Of Pancreatitis-Induced Chylothorax D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


Bilateral Primary Spontaneous Pneumothorax: A Case Report And A Review Of Literature D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


Recurrent Non-Catamenial Hemopneumothorax Secondary To Diaphragmatic And Pleural Endometriosis D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P614 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Spilled Milk: A Case Of Diffuse Chylous Effusions D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P620 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Bilateral Catamenial Pneumothorax D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

RARE PLEURAL TUMORS



More Than Just A Cough — Gastric Adenocarcinoma Presenting With Septal Thickening And Bilateral Pleural Effusions



P375 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Synovial Sarcoma: Masquerading As Massive Pleural Effusion B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


Maleficent Multiple Myeloma: A Case Of Myelomatous Pleural Metastases With Effusion B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P385 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Primary Pleural Lymphoma — Case Report B43: PLEURAL DISEASE CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

35

Rare Disease Term


ADULT

ADULT

Monday, May 20, 2019 P47 9:15 am-4:15 pm

Poster Viewing 11:15 am-1:00 pmOccupational Asbestos Exposure And Malignant Pleural Mesothelioma, Biphasic Type: A Challenging Histopathological And Immunohistochemical Diagnosis

B67: CASE REPORTS: DIAGNOSTIC AND MANAGEMENT DILEMMAS Area A (Hall F, Level 2), KBHCCD


Endobronchial Ultrasound In Diagnosis And Staging Of Malignant Pleural Mesothelioma


P72 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Thoracic Meningioma Metastases: A Single-Center Review B68: ONCOGENIC MUTATIONS, METASTASIS, AND NOVEL

THERAPEUTICS Area A (Hall F, Level 2), KBHCCD



Top2a And Her2neu Evaluation In Malignant Pleural Mesothelioma C110: THE FUTURE OF LUNG CANCER BIOMARKERS: WHERE SHOULD WE LOOK? Arena (Level 2), KBHCCD


P247 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Case Of Primary Pleural Epithelioid Angiosarcoma D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


Myeloid Sarcoma Of The Lung In The Absence Hyperleukocytosis: A Rare Phenomenon D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


The Monster That Burst — When A Mature Teratoma Presents As Pleuritic Chest Pain D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P273 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Cause Of Shortness Of Breath D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P285 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Sarcomatoid Mesothelioma In A Patient With Myelodysplastic Syndrome D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P286 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Ewing Sarcoma Of The Mediastinum D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P302 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Human Herpes Virus-8 Negative Primary Effusion Lymphoma D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P345 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Malignant Solitary Fibrous Tumor Of The Pleura: About A Case D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD

P597 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm What Is This Large Lung Mass? Hint: It’s Not Lung D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

36

Rare Disease Term


ADULT

ADULT


P574 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Grapes Of Wrath: When Uveal Melanoma Targets The Pleura D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P576 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Entity Of Pleural-Based Pulmonary Nodules After Abdominal Trauma D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P276 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Hips Don’t Lie: Myxoid Liposarcoma Mimicking Massive Pulmonary Embolism D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


Proof Is In The Yolk A Unique Case Of Anterior Mediastinal Wideningfrom Yolk Sac Tumor D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

RARE PULMONARY PARENCHYMAL TUMORS


P1118 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Sarcomatoid Carcinoma Of The Lung: A Rare And Unfortunate Disease A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS



Diffuse Large B-Cell Lymphoma Presenting As Progressive Interstitial Lung Disease



A Rock-Solid Lung Mass: A Case Of Rare Inflammatory Myofibroblastic Lung Tumor With Challenging Diagnosis


P1130 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Metastatic Chondrosarcoma Mimicking Pulmonary Embolism A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS



A Brewing Case Of Malt Lymphoma: Primary Pulmonary Lymphoma Presenting As Cystic Lung Disease


P1135 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Rare Tumor: Inflammatory Myofibroblastic Tumor Of The Lungs A70: UNUSUAL PRESENTATIONS AND MIMICS: WHAT YOU SEE IS



Post Obstructive Pneumonia As A Presentation Of A Primary Bronchial Carcinoid Tumor: A Rare Diagnosis In A Young Adult A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD


Bronchus-Associated Lymphoid Tissue (BALT) Lymphoma Presenting As Pneumonia A71: CASE REPORTS: WHEN IN DOUBT LOOK IN THE AIRWAY Area J (Hall F, Level 2), KBHCCD


P958 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Not All That Tree-And-Buds Is Infection B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD

37

Rare Disease Term


ADULT

ADULT



A Case Of Pulmonary Post-Transplant Lymphoproliferative Disorder Diagnosed By Bronchoalveolar Lavage Flow Cytometry



Inflammatory Pseudotumor: How Long Should We Monitor For Recurrence Of Disease?



Atypical Pulmonary Carcinoid And Hyponatremia Should Prompt An Extensive Metastatic Workup



Incidental Primary Pulmonary Mucosa-Associated Lymphoid Tissue Lymphoma



Multi-Modal Treatment Leading To Prolonged Survival In A Patient With Pulmonary Artery Intimal Sarcoma


P106 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Diagnostic Pitfall Of Small Sclerosing Pneumocytoma B69: THORACIC ONCOLOGY: OPTIMIZING DIAGNOSIS AND

MANAGEMENT Area A (Hall F, Level 2), KBHCCD



The Case Of The Mistaken Identity: A Pulmonary Hamartoma That Was Actually An Amyloidoma C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P509 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Inflammatory Myofibroblastic Tumor: A 1 Percenter C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


Respiratory Symptoms In A High-Risk Patient; Do Not Miss Pulmonary Kaposi’s Sarcoma C56: HIV: CLINICAL STUDIES AND BASIC SCIENCE MODELS Area A (Hall F, Level 2), KBHCCD


P237 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Involvement By Intravascular B Cell Lymphoma D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


Pulmonary Nodule In A Low Risk Patient Presenting As An Unexpected Diagnosis D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P244 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Yolk Sac Carcinoma In An Young Adult — Case Report D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P248 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Peripheral Primary Pulmonary Leiomyoma D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

38

Rare Disease Term


ADULT

ADULT


P557 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm An Atypical Presentation Of Pulmonary Kaposi Sarcoma D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P563 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Mastocytosis Manifesting As Chronic Cough D41: COUGH AND IMMUNODEFICIENCIES CASE REPORTS Area D (Hall F, Level 2), KBHCCD

P262 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Extra-Abdominal Desmoid Fibromatosis D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P265 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm An Unusual Case Of A Mediastinal Mass In A Pregnant Woman D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P267 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Decade-Long Ground Glass Opacity Of Mystery D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P270 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Desmoid Fibromatosis Of The Chest: A Case Report D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


Primary Pulmonary Angiosarcoma With Extension Into Left Atrium—Effective Tissue Diagnosis Method D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


A Case Of Pulmonary Sclerosing Pneumocytoma With Multiple Lung And Bone Metastasis D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P299 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Interstitial Lung Disease: Not Always Only Fibrosis D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P260 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm The Spark That Ignited Confusion D61: THORACIC ONCOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD

P274 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Case Of Inflammatory Myofibroblastic Tumor D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P275 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Recurrent Pneumonia Or A Sticky Situation? A Rare Form Of Lung Cancer D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


Small Is Not Always Small. Deception By Nodular Size In The Diagnosis Of Lung Cancer D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

39

Rare Disease Term


ADULT

ADULT



Unique Presentation Of A Rare Neoplasm: Mucoepidermoid Tumor Of The Lung D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P288 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Rare Malignant Nonsmoker Tumor: Lung Sarcoma D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P291 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Carcinosarcoma With Metastasis To Soft Tissue—A Rare Case Report D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


Rare Case Of Uterine Adenosarcoma Metastasis To The Lung 24 Years After Curative Resection D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P312 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm An Unusual Cause Of A Solitary Lung Nodule: A Case Report D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

Primary Pulmonary Malignant Melanoma-Rare Entity D62: THORACIC ONCOLOGY CASE REPORTS II

P293 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Sarcomatoid Carcinoma Of The Lung Presenting As Subcutaneous Nodules D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P295 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Metastatic Hemangiopericytoma Of The Lung D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


A Rare Case Of Primary Hepatoid Adenocarcinoma Of The Lung In A Female Patient D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


Metastatic Endometrial Cancer Presenting As A Pulmonary Nodule After Remote Hysterectomy D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD

P315 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Extra-Nodal Marginal Zone B-Cell Lymphoma: A Case Report D62: THORACIC ONCOLOGY CASE REPORTS II Area C (Hall F, Level 2), KBHCCD


When Antibiotics Fail: Unsuspecting Young Female With Asthma-Like Exacerbations And Recurrent Pneumonias D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD

P349 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm A Fortunate Encounter With A Clinical Mimic D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD


Carcinoid Tumors Of Lung And BRCA Mutations: Is There A Connection Between Them? D63: THORACIC ONCOLOGY CASE REPORTS III Area C (Hall F, Level 2), KBHCCD

40

Rare Disease Term


ADULT

ADULT

RHEUMATOID ARTHRITIS LUNG DISEASE



Prognostic Role Of Blood Kl-6 In Rheumatoid Arthritis-Associated Interstitial Lung Disease A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD

P187 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Characterization Of Airway Disease In Rheumatoid Arthritis A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


Rheumatoid Arthritis’ Clinical Characteristics Stratified By Interstitial Lung Disease Patterns A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


The Design And Rationale Of The Trail Trial: A Randomized Double-Blind Phase Ii Clinical Trial Of Pirfenidone In Rheumatoid Arthritis-Associated Interstitial Lung Disease

A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD



An Incidental Finding Of A Tracheal Bronchus In A Rheumatoid Arthritis Patient: Case Report C36: INTERVENTIONAL PULMONOLOGY CASE REPORTS II Area D (Hall F, Level 2), KBHCCD


Survival Of Patients With Acute Exacerbations Of Rheumatoid Arthritis Associated Interstitial Lung Disease


SCLERODERMA



Relevance Of Accelerated Silicosis In Sandblasters To Rapidly Progressive Pneumoconiosis A26: ENVIRONMENTAL MODIFIERS OF LUNG DISEASE Trinity Ballroom 5-7 (Level 3), Omni

Dallas Downtown


Progressive Massive Fibrosis Contributes To Pulmonary Hypertension In Silicosis A26: ENVIRONMENTAL MODIFIERS OF LUNG DISEASE Trinity Ballroom 5-7 (Level 3), Omni

Dallas Downtown


Electrical Impedance Tomography And Ventilation Heterogeneity On A Silicosis Patient

A47: CRITICAL CARE CASE REPORTS: MECHANICAL VENTILATION FROM NIV TO ECMO Area G (Hall F, Level 2), KBHCCD


ATYR1923 Modulates The Inflammatory Response In Experimental Models Of Interstitial Lung Disease A101: TRANSLATIONAL STUDIES IN ILD, IPF, AND SARCOIDOSIS Room D222-D224 (Level 2), KBHCCD

41

Rare Disease Term


ADULT

ADULT



Quantitative Computed Tomography In Systemic Sclerosis-Associated Interstitial Lung Disease: A Densitometric Assessment Of Disease Severity

A108: PATHOPHYSIOLOGY IN DIFFUSE PARENCHYMAL LUNG DISEASES Ballroom D Four (Level 3), KBHCCD

P179 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Biomarkers In Systemic Sclerosis Associated Interstitial Lung Disease A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


Predictors For The Development Of Systemic Sclerosis Associated Interstitial Lung Disease (SSC-ILD) — Data From The German SSC-Network A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


The Place Of Respiratory Manifestations During Scleroderma In Dakar: A Multicentric Study A37: CONNECTIVE TISSUE DISEASE-INTERSTITIAL LUNG DISEASE Area B (Hall F, Level 2), KBHCCD


A New Era In Scleroderma Interstitial Lung Disease And Renal Crisis: Rationale For Early Use Of Endothelin Receptor Antagonists A40: INFLAMMATORY DPLDs CASE REPORTS Area D (Hall F, Level 2), KBHCCD



Circulating Krebs Von Den Lungen And CC Chemokine Lligand 2 Predict Progression Of Interstitial Lung Disease In Systemic Sclerosis Patients Undergoing Immunosuppressive Therapy

B103: ILD: THERAPY Room C140/C142 (Level 1), KBHCCD

P318 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Anthracosilicosis: A Rare Cause Of Endobronchial Tumor B41: INTERVENTIONAL PULMONOLOGY CASE REPORTS I Area C (Hall F, Level 2), KBHCCD


Interstitial Lung Disease And Pulmonary Hypertension In Systemic Sclerosis: A Real-World Experience B55: USE YOUR ILLUSION I: CLINICAL RESEARCH IN PAH Area G (Hall F, Level 2), KBHCCD


Nintedanib Reduces Lung Function Decline In Patients With Systemic Sclerosis-Associated Interstitial Lung Disease: Results Of The Senscis Trial B17: ADVANCES IN ILD THERAPY Room C155-C156 (Level 1), KBHCCD



Feasibility And Efficacy Of Cohort Enrichment For Progressive Lung Fibrosis In Systemic Sclerosis — An EUSTAR Database Analysis



Prediction And Frequency Of Progressive Lung Fibrosis In Patients With Systemic Sclerosis-Associated Interstitial Lung Disease In The World’s Largest Database Of Patients With Systemic Sclerosis (EUSTAR)


42

Rare Disease Term


ADULT

ADULT

Tuesday, May 21, 2019 124 2:15 pm-4:15 pm

Poster Viewing 2:15 pm-2:45 pmPoster Discussion 2:45 pm-4:15 pm

Expert Consensus On The Screening, Treatment, And Management Of Patients With Systemic Sclerosis-Associated Interstitial Lung Disease (SSC-ILD), And The Potential Future Role Of Anti-Fibrotics In A Treatment Paradigm For SSC-ILD: A Delphi Consensus Study



Gene Expression Of Peripheral Blood Monocytes In Systemic Sclerosis Associated Interstitial Lung Disease C34: ILD AND IPF: CLINICAL AND MECHANISTIC STUDIES Area H (Hall F, Level 2), KBHCCD

P583 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Heart Rate Recovery In Patients With Scleroderma C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD


Antifibrotic Efficacy Of Nintedanib In A Cellular Model Of Scleroderma Associated Interstitial Lung Disease C62: FIBROBLAST BIOLOGY Area C (Hall F, Level 2), KBHCCD

P422 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Osteoclast-Like Differentiation In Mouse Model Of Silicosis C64: PULMONARY FIBROSIS MODELS AND MECHANISTIC

INSIGHTS Area C (Hall F, Level 2), KBHCCD



Nintedanib In Patients With Systemic Sclerosis-Associated Interstitial Lung Disease (SSC-ILD): The Senscis Trial



Scleroderma-Related Mortality In The United States From 2003 To 2016 D24: AUTOIMMUNE DISEASE, DRUG-INDUCED, AND TRANSPLANT Room C140/C142 (Level 1), KBHCCD


Single-Cell Analysis Reveals Fibroblast Heterogeneity And Myofibroblasts In Systemic Sclerosis-Associated Interstitial Lung Disease D29: LUNG MULTI-OMICS TO MECHANISM Room D222-D224 (Level 2), KBHCCD


Circulating Mitochondrial DNA Is Associated With Fibroblast Activation And Disease Progression In Scleroderma Associated Interstitial Lung Disease

D107: MITOCHONDRIA AND ER STRESS IN HOMEOSTASIS AND REPAIR Ballroom D Three (Level 3), KBHCCD

VASCULITIS



Off-Label Use Of Benralizumab For Severe Eosinophilic Granulomatosis With Polyangiitis B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD

43

Rare Disease Term


ADULT

ADULT


P266 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Anca Negative Eosinophilic Granulomatosis With Polyangiitis B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD

P237 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Anti GBM Disease: A Case Report B40: AUTOIMMUNE LUNG DISEASE CASE REPORTS Area C (Hall F, Level 2), KBHCCD

P939 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Dilemma Of Massive Hemoptysis And Thrombosis: Hughes-Stovin Syndrome B54: CASE REPORTS IN PULMONARY VASCULAR MEDICINE II Area G (Hall F, Level 2), KBHCCD


P439 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Trimethoprim/Sulfamethoxazole In Induced Alveolar Hemorrhage C38: AUTOIMMUNE, DRUG RELATED, AND TRANSPLANT Area D (Hall F, Level 2), KBHCCD

P439 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Cryoglobulinemic Vasculitis: A Rare Cause Of Diffuse Alveolar Hemorrhage C33: CASE REPORTS IN AUTOIMMUNE AND INFLAMMATORY




Burden Of Illness Associated With Eosinophilic Granulomatosis With Polyangiitis (EGPA, Formerly Churg-Strauss Syndrome) In The United States: Evidence From Two Administrative Claims Databases


YELLOW NAIL SYNDROME


P604 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Yellow Nail Syndrome (YNS) D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

P617 9:15 am-3:30 pmPoster Viewing 11:15 am-1:00 pm Yellow (Toe)Nail Syndrome D42: PLEURAL DISEASE CASE REPORTS II Area D (Hall F, Level 2), KBHCCD

44

Rare Disease Term


PEDIATRIC

PEDIATRIC

ABCA3 ASSOCIATED ILD



ABCA-3 Related Surfactant Dysfunction Presenting As Neonatal Respiratory Failure And Clinical Improvement With Supportive Care

C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL MALFORMATIONS, AND MORE Area E (Hall F, Level 2), KBHCCD


More Than BPD? Diagnosis, Prognosis And Treatment Of ABCA3 Deficiency In An Extremely Premature Infant.


P761 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Not All ABCA3 Mutations Are Created Equal C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL

MALFORMATIONS, AND MORE Area E (Hall F, Level 2), KBHCCD

9:15 am-11:15 amPoster Viewing 9:15 am-9:45 amPoster Discussion 9:45 am-11:15 am

Cre Recombinase-Mediated, Site-Specific Integration For Functional Characterization Of ABCA3 Variants C18: RARE LUNG DISEASES Room D220/D227 (Level 2), KBHCCD

ACD-MPV (ALVEOLAR CAPILLARY DYSPLASIA WITH MISALIGNMENT OF THE PULMONARY VEINS)



Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins (ACDMPV): A Case Series



Synchrotron Phase Contrast Micro-Ct As A Novel Tool For Understanding Pulmonary Vascular Pathobiology And The 3D Micro-Anatomy Of Alveolar Capillary Dysplasia With Misaligned Pulmonary Veins

C49: TICKET TO RIDE: EXPERIMENTAL MODELS OF PAH Area J (Hall F, Level 2), KBHCCD

AV MALFORMATION



Vascular Malformations With Hemoptysis: Don’t Know Which Treatment To PIK? Use Sirolimus! C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

BRONCHIOLITIS OBLITERANS



Clinical Study By Tonifying Lung And Spleen,Phlegm And Dispelling Stasis Method In Treatingchildren With Bronchiolitis Obliterans

A53: CLINICAL STUDIES IN NEONATAL AND PEDIATRIC LUNG DISEASE AND CYSTIC FIBROSIS Area D (Hall F, Level 2), KBHCCD



Pediatric Hematopoietic Stem Cell Transplant Patients’ Six-Minute Walk Test Distance Declines At Day 100 But Returns To Baseline By 1-Year Post Transplant

C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE


45

Rare Disease Term


PEDIATRIC

PEDIATRIC



129XE MRI And Six Minute Walk Test Correlations In Pediatric Patients After Hematopoietic Stem-Cell Transplantation




Bronchiolitis Obliterans Secondary To Steven Johnson Syndrome, Diagnostic And Therapeutic Challenges C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


Cryptogenic Organizing Pneumonia, A Rare Cause Of Pulmonary Nodules In Children: A Case Report C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

CATAMENIAL HEMOPTYSIS


P676 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Catamenial Hemoptysis In A 16- Yo African American Female C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

CHILDHOOD INTERSTITIAL LUNG DISEASES — CONNECTIVE TISSUE DISEASE



Progression Of Lung Disease In A Child With STING-Associated Vasculopathy With Onset In Infancy C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

P664 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm STAT5b Deficiency: A Rare Cause Of Pulmonary Alveolar Proteinosis C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


The Use Of Tofactinib, Chronic Ventilation, And Long Term VV-ECMO In A Pediatric Patient With Rapidly Progressive Interstitial Lung Disease From MDA5+ Juvenile Dermatomyositis

C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

P668 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Manifestations Of Inflammatory Bowel Disease: A Case Report C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


Pediatric Interstitial Lung Disease And Pneumomediastinum In Clinically Amyopathic Juvenile Dermatomyositis: Treatment With Pirfenidone As An Adjuvant


CHILDHOOD INTERSTITIAL LUNG DISEASES — OTHER



In Vitro Analysis Of Alloreactivity And Tolerance In Bilateral Orthotopic Lung Transplant (BOLT) In Tandem With Bone Marrow Transplant (BMT) Recipients


46

Rare Disease Term


PEDIATRIC

PEDIATRIC


P661 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Not So Simple Explanation Of Dyspnea In A 12-Year Old C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


Infant Lung Transplantation In Suspected Case Of Surfactant Protein Deficiency



Importance Of The Study Of The Lamelar Bodies In Respiratory Failure Of The Newborn



The Diagnostic Challenge Of Nonspecific Interstitial Pneumonia In A Pediatric Patient C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


Progression Of Alveolar Simplification To End-Stage Fibrotic Lung Disease In Childhood C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


A Novel Interstitial Lung Disease Associated With Systemic Juvenile Idiopathic Arthritis: Characteristics And Risk Factors




Treatment Of Interstitial Lung Disease In STAT3 Gain-Of-Function Using JAK Inhibitors




Evaluation Of Inter-Observer Variation For CT Identification Of Childhood Interstitial Lung Disease




Genomic Susceptibility To The Development Of Pediatric Interstitial Lung Disease C31: TRANSLATIONAL STUDIES IN SARCOIDOSIS Area C (Hall F, Level 2), KBHCCD


Bilateral Lung Transplantation In A 9-Year-Old Girl With Pulmonary Hypertension Associated With Severe Bronchopulmonary Dysplasia


CONGENTIAL ACINAR DYSPLASIA



Congenital Acinar Dysplasia: Familial Cause Of Severe Primary Lung Hypoplasia


47

Rare Disease Term


PEDIATRIC

PEDIATRIC

CONGENITAL CENTRAL HYPOVENTILATION SYNDROME


Poster Viewing 11:15 am-1:00 pmPositional Impairment Of Gas Exchange During Diaphragm Pacing Alleviated By Increasing Amplitude Settings In A Girl With Congenital Central Hypoventilation Syndrome

C47: CASE REPORTS: PEDIATRIC CYSTIC FIBROSIS, LUNG INFECTION, AND SLEEP DISORDERED BREATHING Area E (Hall F, Level 2), KBHCCD


Early Diagnosis Non-Invasive Management In A Newborn With Classic Congenital Central Hypoventilation Syndrome



Congenital Central Hypoventilation Syndrome In An Infant With Multiorgan System Failure


CONGENITAL DIAPHRAGMATIC HERNIA

Sunday, May 19, 2 019


The Health Related Quality Of Life Of Caregivers Of Children With Congenital Diaphragmatic Hernia




Clinical Features And Outcomes Associated With Tracheostomy In Congenital Diaphragmatic Hernia

B26: CLINICAL STUDIES IN PEDIATRIC SLEEP, HOME VENTILATION AND NEUROMUSCULAR DISEASE




Proteomic Profiling Of Tracheal Fluid In Ovine Model Of Congenital Diaphragmatic Hernia With Fetal Tracheal Occlusion Identifies Dysregulation Of Epithelial PI3K/AKT, WNT, And NOTCH Signaling

C28: PATHWAYS OF LUNG MORPHOGENESIS Ballroom D Three (Level 3), KBHCCD

CYSTIC AND BULLOUS LUNG DISEASES — OTHER


P673 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Large Bullous Lung Disease In A Child With Proteus Syndrome C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


Subxyphoid Uniport Video-Assisted Thoracic Surgery For A 13-Month-Old Infant: The Minimum Age Record Of Pumonary Cysts Operation


DIFFUSE ALVEOLAR HEMORRHAGE


Poster Viewing 11:15 am-1:00 pmSuccessful Induction Treatment With Rituximab Of Isolated Pauci-Immune Pulmonary Capillaritis Presenting As Diffuse Alveolar Hemorrhage In A Pediatric Patient


48

Rare Disease Term


PEDIATRIC

PEDIATRIC


Poster Viewing 11:15 am-1:00 pmHypocomplementemic Urticarial Vasculitis Syndrome With Diffuse Alveolar Hemorrhage, Bronchiectasis, And Progressive Obstructive Pulmonary Disease In An 8 Year-Old Boy


DUCHENNE MUSCULAR DYSTROPHY



Comparable Rates Of Progressive Decline In Left Ventricular Function And Pulmonary Function In Children With Duchenne Muscular Dystrophy





Mri Assessment Of Diaphragm Impairment In Duschenne Muscolar Distrophy (DMD): Comparison To Optoelectronic Plethysmography And Pulmonary Function Tests (PFTS)

C109: RESPIRATORY MUSCLE DYSFUNCTION: MECHANISM AND ASSESSMENT Ballroom D Four (Level 3), KBHCCD


Application Of Machine Learning Tools Using Lung Function Tests To Predict The Age Of Permanent Wheelchair Dependence In Children With Duchenne Muscular Dystrophy

C67: LUNG FUNCTION TEST Area G (Hall F, Level 2), KBHCCD

EOSINOPHILIC DISORDERS — PULMONARY



Induction Of Remission Following Treatment With Benralizumab In A 16-Year-Old Male With Eosinophilic Granulomatosis With Polyangiitis C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

P690 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Eosinophilic Pneumonia In A Pediatric Lung Transplant Patient C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

FILAMIN A GENE MUTATION RELATED INTERSTITIAL LUNG DISEASE


P659 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Novel Filamin A Mutation Related Interstitial Lung Disease In An Infant C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

GLYCOGEN STORAGE AND METABOLIC DISORDERS



Saber-Sheath Airway With Multiple Areas Of Tracheal Stenosis Caused By Mucolipidosis Type II


HAMMAN’S SYNDROME


P741 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Swollen Child With A Cough C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


49

Rare Disease Term


PEDIATRIC

PEDIATRIC

HERMANSKY-PUDLAK SYNDROME



Characterization Of Pulmonary Function In Children With Hermansky-Pudlak Syndrome




Alveolar Epithelial Type 2 Cell Dysfunction In Hermansky-Pudlak Syndrome Type 2 Patient-Derived Induced Pluripotent Stem Cells


HYPERSENSITIVITY PNEUMONITIS



Lentil Aspiration Causing Hypersensitivity Pneumonitis: Describing A Novel Antigen, Novel Entity


LANGERHANS CELL HISTIOCYTOSIS



Pulmonary Involvement Of Langerhans Cell Histiocytosis As Initial Manifestation Of The Disease In A Pediatric Patient: A Case Report C69: LUNG CANCER Area G (Hall F, Level 2), KBHCCD

LYMPHATIC ANOMALIES: GENERALIZED LYMPHATIC ANOMALY (GLA), GORHAM-STOUT DISEASE (GSD)



Abnormal Pulmonary Lymphatic Flow In Patients With Lymphatic Anomalies And Respiratory Compromise On MR Lymphangiogram



P752 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Central Conducting Lymphatic Anomaly Leading To Respiratory Failure C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


LYMPHATIC ANOMALIES: GORHAM-STOUT DISEASE


P727 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A 15-Year-Old With Dyspnea And Vanishing Bones C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


NEUROENDOCRINE CELL HYPERPLASIA OF INFANCY


Poster Viewing 11:15 am-1:00 pmIntersection Of Aerodigestive And Childhood Interstitial Lung Disease Evaluations: Infant Neuroendocrine Cell Hyperplasia Disguised By Aspiration And Type 1 Laryngeal Cleft


50

Rare Disease Term


PEDIATRIC

PEDIATRIC



Home High Flow Nasal Cannula As A Novel Therapy For Improvement Of Severe OSA In A Child With NEHI


NON-CF BRONCHITECTASIS


P688 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A 7 Year-Old-Female With Bronchiectasis Found To Have RAG1 Mutations C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

NON-TUBERCULOUS MYCOBACTERIAL INFECTION — PULMONARY



Evolutionary Phylogenomics Identified Hypermutable Isolates Of Nontuberculous Mycobacteria In A Cystic Fibrosis Chronic Infection

D34: CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Area F (Hall F, Level 2), KBHCCD

ORGANIZING PNEUMONIA



The Many Faces Of Cytomegalovirus Infection In The Bone Marrow Transplanted Lungs

C57: VIRAL LUNG INFECTION CLINICAL STUDIES AND CASE REPORTS Area A (Hall F, Level 2), KBHCCD

PLASTIC BRONCHITIS


P719 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Hypoplastic Heart And Plastic Lungs C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


PRIMARY CILIARY DYSKINESIA



Preserved Ciliary Defects In Airway Epithelia Derived From Primary Ciliary Dyskinesia Basal Cells Expanded In 3T3-J2 Co-Culture A61: EPITHELIAL BIOLOGY: Area C (Hall F, Level 2), KBHCCD


910 2:15 pm-4:15 pm Poster Viewing 2:15 pm-2:45 pmPoster Discussion 2:45 pm-4:15 pm

Sensitivity Of Multiple Breath Washout And Spirometry For Detection Of Early Lung Disease In Children With Primary Ciliary Dyskinesia And Cystic Fibrosis: A Multicenter Study

C104: THE MODERN PEDIATRIC PULMONARY FUNCTION LAB: NEW STANDARDS AND NEW TESTS



Primary Ciliary Dyskinesia (PCD) Diagnostic Testing Before And After Establishment As A PCD Clinical Center




Ciliary Biopsy Quality Improvement: Before And After Establishment Of A Primary Ciliary Dyskinesia (PCD) Clinical Center



51

Rare Disease Term


PEDIATRIC

PEDIATRIC



Primary Ciliary Dyskinesia (PCD) Registry In Alberta C25: CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE


920 9:15 am-11:15 amPoster Viewing 11:15 am-1:00 pm

Recessive DNAH9 Loss-Of-Function Mutations Cause Absence Of ODAS Type 2 And Only Subtle Respiratory Ciliary Beating Defects



Wednesday, May 22, 2019 P839 9:15 am-3:30 pm

Poster Viewing 11:15 am-1:00 pmIncreased NADPH In Human PCD Airway Epithelial Cells: Does The Reducing Environment In Cells With Ciliary Dysfunction Lead To Decreased No Evolution?

D34: CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Area F (Hall F, Level 2), KBHCCD

PROTEUS SYNDROME


P724 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Manifestations, Management Of Proteus Syndrome C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


PULMONARY ALVEOLAR PROTEINOSIS


P122 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Characterization Of Murine Delivery Of Aerosolized Therapeutics A45: CRITICAL CARE: OF MICE AND MEN — INSIGHTS FROM

EXPERIMENTAL AND ANIMAL MODELS IN ARDS AND SEPSIS Area A (Hall F, Level 2), KBHCCD


2:15 pm-4:15 pmOral Presentation 2:45 pm-3:00 pm

CRISPR/CAS9 Genome Editing Therapy For Hereditary Pulmonary Alveolar Proteinosis B94: BEST OF PEDIATRICS Dallas Ballroom G (Level 3), Omni

Dallas Downtown



Lobar Or Segmental Bronchoscopic Lavage As A Novel Treatment For Pulmonary Alveolar Proteinosis In The Pediatric Population C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


A Case Of Pediatric Autoimmune Pulmonary Alveolar Proteinosis That Has Been Refractory To 'Standard' Treatment C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


Combined Use Of Whole Lung Lavage And Inhaled Sargramostim For Lysinuric Protein Intolerance–Associated Pulmonary Alveolar Proteinosis Ina 13 Year-Old Male


RARE PULMONARY VASCULAR DISEASE



Prominentintrapulmonary Bronchopulmonary Anastomoses In Children With Single Ventricle Heart Disease


52

Rare Disease Term


PEDIATRIC

PEDIATRIC

RARE CONGENITAL ANOMALIES



Therapy At 30 Days Of Life Predicts Lung Function At 6–12 Months In Infants With Congenital Diaphragmatic Hernia



P731 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Metastases In Attenuated Familial Adenomatous Polyposis C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL



A Case Of Bilateral Pulmonary Varices Associated With Hybrid Left Pulmonary Cpam And Sequestration In A 2 Year-Old Girl



Dehydrated Hereditary Stomatocytosis Causing Severe Ascites Leading To Pulmonary Hypoplasia And Respiratory Insufficiency In A Neonate



Unilateral Lung Agenesis And Exercise Test Findings In A Previously Well Adolescent Female


P749 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Unilateral Pulmonary Agenesis With Asthma C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL



Sub-Carinal Bronchogenic Cyst Presenting With Recurrent Pleural Effusion In A Ten Year Old Boy


P756 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm De Novo Variant Of The SAMD9 Gene: Mirage Syndrome C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


P757 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm A Rare Case Of Esophageal Lung With Systemic Arterial Supply C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL



Congenital Non-Isolated Arhinia: A Unique Case With Multi-Organ Involvement C72: CASE REPORTS OF RARE DISEASES Area G (Hall F, Level 2), KBHCCD

RARE PULMONARY VASCULAR DISEASE


P725 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Looking For Causes Of Chronic Hypoxemia C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


53

Rare Disease Term


PEDIATRIC

PEDIATRIC

RARE TUMORS — AIRWAY



Because Not Everything Is Asthma, Bronchial Mucoepidermoid Carcinoma In Pediatrics



A Tricky Diagnosis Of Mucoepidermoid Carcinoma In An Adolescent From A Tb Endemic Country


P733 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Primary Mucoepidermoid Carcinoma Of The Lung In A Child C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


P734 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Rare Asthma Mimic In A 15-Year Old C48: CASE REPORTS: NEONATAL LUNG DISEASE, CONGENITAL


RARE TUMORS — PARENCHYMAL



Not All Mixed Cystic And Solid Lung Lesions Are Congenital Pulmonary Malformations: A Case Of An Isolated Pulmonary Infantile Hemangioma


SICKLE CELL DISEASE



Immune Response To Pneumococcal Polysaccharide Vaccine In Children With Sickle Cell Disease



Estimation Of Pulmonary Capillary Blood Volume And Its Relation To Lung Volumes In Children With Sickle Cell Disease

C104: THE MODERN PEDIATRIC PULMONARY FUNCTION LAB: NEW STANDARDS AND NEW TESTS


P1250 9:15 am-11:15 amPoster Viewing 9:15 am-9:45 amPoster Discussion 9:45 am-11:15 am

Retrospective Cohort Study Of Asthma Management In Pediatric Patients With Sickle Cell Disease




Nocturnal Hypoxemia Measured By Polysomnogram Is Associated With Acute Chest Syndrome In A Pediatric Sickle Cell Disease Population



54

Rare Disease Term


PEDIATRIC

PEDIATRIC

SPINAL MUSCULAR ATROPHY



Respiratory Assessments And Sleep Related Breathing Disorders In Children With Spinal Muscular Atrophy

A69: SRN: WHAT CAN WE LEARN FROM CLINICAL AND EPIDEMIOLOGICAL STUDIES IN SLEEP? Area K (Hall F, Level 2), KBHCCD



Treatment Of Spinal Muscular Atrophy With Nusinersen Produces Improvement In Pulmonary Function In Children With SMA II And SMA III




Characteristics Of Sleep Disordered Breathing In Pediatric Spinal Muscular Atrophy

B53: SLEEP DISORDERED BREATHING AND LONG-TERM VENTILATION IN PEDIATRICS Area K (Hall F, Level 2), KBHCCD

SURFACTANT PROTEIN C ASSOCIATED ILD



Expression Of A Prototypical Surfactant Protein C Brichos Mutation Causes Epithelial Er Stress, Spontaneous Lung Injury And Fibrotic Remodeling A29: EMERGING CONCEPTS IN LUNG FIBROSIS Ballroom D Four (Level 3), KBHCCD



Chest CT Analysis For Features Of Fibrosis In Children With SpC Genetic Mutations



SWYER-JAMES-MACLEOD SYNDROME



Acute Onset Of Swyer-James-Macleod Syndrome Following Adeno Virus In Infancy C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

TBX4 ASSOCIATED DISEASE



The Transcription Factor TBX4 Regulates The Expression Of CYP1B1 D106: PICK YOUR POISON: GENES, DRUGS, AND PAH Ballroom A Four (Level 2), KBHCCD

THORACIC ENDOMETRIOSIS/CATAMENIAL PNEUMOTHORAX


P656 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Chief Complaint: Coughing Up Blood Monthly! C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

55

Rare Disease Term


PEDIATRIC

PEDIATRIC

VASCULITIS — ANCA ASSOCIATED



Pulmonary Manifestations And Outcomes In Anca Associated Vasculitides: A Single Center Experience



VASCULITIS — GRANULOMATOSIS WITH POLYANGIITIS (GPA)



Granulomatosis With Polyangiitis In A Pediatric Patient Presented With Bell’s Palsy And Pulmonary Involvement C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

VASCULITIS — OTHER


P436 9:15 am-4:15 pmPoster Viewing 11:15 am-1:00 pm Pulmonary Manifestations Of Behcet's Disease C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD


It’s Not The Heart: An Unusual Case Of Medium Vessel Vasculitis And Pulmonary Hypertension C46: CASE REPORTS: PEDIATRIC DIFFUSE LUNG DISEASE Area E (Hall F, Level 2), KBHCCD

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