cjd and kuru: prion viruses by: danny nemeth. prion infectious agent composed of protein in a...
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CJD and Kuru: Prion CJD and Kuru: Prion VirusesViruses
By: Danny NemethBy: Danny Nemeth
PrionPrion
infectious agent composed of protein in a infectious agent composed of protein in a misfolded formmisfolded form
CJDCJD
Creutzfeldt-Jakob DiseaseCreutzfeldt-Jakob Diseaseneurodegenerative disorderneurodegenerative disorderyear of onset of illness year of onset of illness
StructureStructure
no Nucleic acidsno Nucleic acidsmass of 27,000 - 30,000 daltons mass of 27,000 - 30,000 daltons 145 amino acids145 amino acidsStructure unknownStructure unknown
CauseCause
promotes refolding of native proteins promotes refolding of native proteins mass of misfolded proteins disrupts cell mass of misfolded proteins disrupts cell
functionfunction
ALWAYS FATAL!ALWAYS FATAL!
SymptomsSymptoms
Neurological Neurological DepressionDepressionConfusionConfusion loss of coordination and balanceloss of coordination and balance progressive blindness progressive blindness
Transmission Transmission
GENETICS! GENETICS! Defective HGHDefective HGHCANNIBALISM! CANNIBALISM!
KURUKURU
Misfolded ProteinsMisfolded Proteins
CannibalismCannibalismBrainsBrains
SymptomsSymptoms
Coordination problemsCoordination problems Difficulty walking Difficulty walking Swallowing difficultySwallowing difficulty Tremors and muscle jerks Tremors and muscle jerks
Treatment and PrognosisTreatment and Prognosis•NONE!
•Prognosis
•Death after 1 year of symptoms
Stuff I UsedStuff I Used
http://www.cjdsurveillance.com/http://www.cjdsurveillance.com/abouthpd.htmlabouthpd.html
http://www.cdc.gov/ncidod/dvrd/cjd/http://www.cdc.gov/ncidod/dvrd/cjd/index.htmindex.htm
http://en.wikipedia.org/wiki/Kuru_(disease)http://en.wikipedia.org/wiki/Kuru_(disease)http://en.wikipedia.org/wiki/Creutzfeldthttp://en.wikipedia.org/wiki/Creutzfeldt
%E2%80%93Jakob_disease%E2%80%93Jakob_diseasehttp://www.ncbi.nlm.nih.gov/http://www.ncbi.nlm.nih.gov/
pubmedhealth/PMH0002355/pubmedhealth/PMH0002355/