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Female Genital Development Female Genital Development Richard Schlussel M.D. Assistant Professor Department of Urology Columbia University

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Page 1: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Female Genital DevelopmentFemale Genital DevelopmentRichard Schlussel M.D.

Assistant ProfessorDepartment of Urology

Columbia University

Page 2: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

• Normal development• Duplication• Agenesis• UG Sinus• Imperforate hymen• CAH

Page 3: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 4: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 5: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 6: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 7: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 8: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Hypospadias

Page 9: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Hypospadias repair

Page 10: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Hypospadias repair

Page 11: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

• Paramesonephric duct– A.K.A. Mullerian Duct– Becomes future

• Fallopian tubes• Uterus• Upper 2/3 vagina

Page 12: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 13: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

VAGINAL AND UTERINEDUPLICATION

Page 14: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Bicornuate Uterus

Page 15: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Didelphys uterus

Page 16: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Unicornuate Uterus

Page 17: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Complete Vaginal Duplication

• Symptom– Blood persists despite

tampon duringmenses

Page 18: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

• Symptom– Upper vagina fills

with blood duringmenses

Page 19: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 20: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Mayer-Rokitansky-Küster-Hauser Syndrome

1 in 5,000births

Page 21: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

VAGINALAGENSIS

Page 22: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 23: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 24: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Normal Hymenal Ring

Page 25: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Imperforate hymen

Mucous due to maternalhormones

Page 26: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

Intra-op drainage of imperf hymen

Page 27: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

UROGENITAL SINUS

Page 28: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

UROGENITAL SINUS

Page 29: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

X X

CONGENITAL ADRENAL HYPERPLASIA (CAH)

Page 30: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

CAH 46 XX

Page 31: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 32: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 33: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 34: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 35: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 36: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,
Page 37: Female Genital Development - Columbia University · Complete Vaginal Duplication ... –Renal agenesis ... (Distal) Middle Posterior (Proximal) by Saunders, copyright 2007 by Saunders,

• Association withUrinary TractAnomalies– Renal agenesis– Ectopic ureters