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Page 1: Genetic Disorders Among Arab Populations ||  || Front_matter

Genetic Disorders Among Arab Populations

Page 2: Genetic Disorders Among Arab Populations ||  || Front_matter

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Page 3: Genetic Disorders Among Arab Populations ||  || Front_matter

Ahmad S. TeebiEditor

Genetic Disorders AmongArab Populations

Second Edition

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EditorAhmad S. TeebiWeill Cornell Medical College in QatarQatar FoundationDohaEducation [email protected]

First edition published by Oxford University Press, 1997.

ISBN 978-3-642-05079-4 e-ISBN 978-3-642-05080-0DOI 10.1007/978-3-642-05080-0Springer Heidelberg Dordrecht London New York

Library of Congress Control Number: 2010932676

# Springer-Verlag Berlin Heidelberg 2010This work is subject to copyright. All rights are reserved, whether the whole or part of the material isconcerned, specifically the rights of translation, reprinting, reuse of illustrations, recitation, broadcasting,reproduction on microfilm or in any other way, and storage in data banks. Duplication of this publicationor parts thereof is permitted only under the provisions of the German Copyright Law of September 9,1965, in its current version, and permission for use must always be obtained from Springer. Violationsare liable to prosecution under the German Copyright Law.The use of general descriptive names, registered names, trademarks, etc. in this publication does notimply, even in the absence of a specific statement, that such names are exempt from the relevant protectivelaws and regulations and therefore free for general use.

Cover design: WMXDesign GmbH, Heidelberg, Germany

Printed on acid-free paper

Springer is part of Springer Science+Business Media (www.springer.com)

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To my parents, brothers and sisters, and my children Saeed, Basel, Asil and Asmaand the whole Arab Family.

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Acknowledgements

The editor is grateful to the authors of the individual chapters who welcomed the

initiative and were keen to provide their contributions on time. Special thanks to

Professor Charles R. Scriver, who made the effort to write the foreword to this

book. I am thankful to my wife Mrs. Amal Teebi for her encouragement and support

and to Saeed Teebi for his assistance in some parts of the manuscript.

The assistance of Mrs. Mariette D’ Souza, Gemma Fabricante and Martin

Marion from Weill Cornell Medical College in Qatar, in preparation of some

chapters and maps, is greatly appreciated.

I express my gratitude also to Springer press and in particular to Andrea Pillman

and Ursula Gramm for their help in the publication of this book.

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Foreword

Genetic Disorders among Arab Populations by Ahmad S. Teebi and co-authors

appears here in its second edition. The first edition (in 1997) shows how one could

tap into a rich load of information on human and medical genetics, a source

probably too little mined until now. One can be pleased that the first edition was

warmly welcomed by Prof. Victor McKusick, the author of the Foreword to that

edition. The authors of this edition have taken pains to remind us again that persons

and patients, and the corresponding families and communities, represent a stream of

human history and a region of the world that embraces ethnic, cultural and religious

attributes more diverse than we might have imagined, yet with a commonality that

gives “coherence to an account of it and a usefulness [when it is considered] as a

unit” (VA McKusick, Foreword to first edition).

Arab populations have their repertoire of genetic disorders, both universal and

particular. Genetic diversity within these source populations, along with the fact

that rates of inbreeding are often high and family sizes are often large, constitutes

conditions that facilitate the emergence and detection of phenotypes explained

notably by autosomal recessive inheritance, in which case, the use of homozygosity

gene mapping will facilitate discovery of the corresponding genes. Meanwhile, the

interval between the publication of the first and second editions of genetic disorders

has witnessed emergence of the Middle East Genetic Association of America and

the creation of ethnic (Arabic)-related, locus-specific mutation databases to serve as

nodes in the network of related interests. Driven by relevant research interests,

initiatives are emerging in the Arabic world to address issues such as taxonomy and

fine-grained descriptions of variant disease phenotypes, their origins, distributions

and frequencies in populations, their molecular infrastructure, and with a better

knowledge of their pathogenetic processes, better opportunities to address coun-

seling, prevention and treatment.

The authors of the second edition have again chosen not to provide an exhaustive

list of relevant genetic disorders; that can be done eventually when there is a curated

online database. Rather, the authors again highlight various issues and perspectives

that can be seen through the windows offered by a number of prevalent genetic

disorders in the Arabic world. Accordingly, the attitudes and responses generated

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by these problems, as they are influenced by Islamic perspectives, wisely constitute

the recurrent underlying theme in the book, because the cultures and faith of the

Arabic communities yield quite different responses and perspectives from the

corresponding encounters in the non-Islamic world. It is a particular form of a

larger issue attracting notice (viz. Suther and Kiros, Genet Med 11:655–662, 2009;

Krotoski et al. Genet Med 11:663–668, 2009).

The authors use prevalent, pan-Arabic disorders (Table 1.1), along with a

selection of rarer “founder” disorders (Table 1.2), to delve into the biological

explanations for their occurrence and impact. These disorders set the scene to

explain important demographic issues, the related population dynamics, indicators

of individual collective health, and the impacts of endogamy and consanguinity on

the frequencies and distribution of the disorders. Familial Mediterranean Fever, for

example, illustrates these perspectives well and is highlighted accordingly. The

authors examine 15 different countries and regions harbouring Arabic populations,

to discern issues with more specific aspects. One might say that in this diversity,

there is a unity and vice versa. Consolidations of the expanding information on

genetic disorders in Arabic populations improves our knowledge of them. Whether

that leads to better wisdom, in how we help the individuals, families and commu-

nities harboring them, is, I am convinced, a sincere motivation to pursue the course

undertaken by Professor Teebi and his co-authors. It has indeed yielded this

enhanced second edition of Genetic Disorders among Arab Populations.

Charles R. Scriver MDCM FRS

Alva Professor Emeritus of Human Genetics

Professor of Pediatrics and Biology

McGill University

Montreal, Canada

x Foreword

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Contents

Part I Introduction

1 Introduction: Genetic Diversity Among Arabs . . . . . . . . . . . . . . . . . . . . . . . . . . 3

Ahmad S. Teebi

Part II Demography, Economy, and Genetic Services in Arab Countries

2 Arab Demography and Health Provision . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 37

Sulayman S. Al-Qudsi

3 Influences of Systems’ Resources and Health Risk Factors on Genetic

Services . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 65

Amal A. Saadallah and Ahmad S. Teebi

4 Endogamy and Consanguineous Marriage in Arab Populations . . . . . . 85

Alan H. Bittles and Hanan A. Hamamy

Part III Selected Disease Entities Prevalent Among the Arabs

5 Familial Mediterranean Fever and Other Autoinflammatory

Disorders . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 111

Hatem El-Shanti and Hasan Abdel Majeed

6 Muscular Dystrophies and Myopathies in Arab Populations . . . . . . . . . 145

Mustafa A.M. Salih

7 New Syndromes First Reported Among Arabs . . . . . . . . . . . . . . . . . . . . . . . . 181

Ahmad S. Teebi

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Part IV Genetic disorders in Arab Countries Geographic Regions

8 Genetic Disorders in Egypt . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 219

Samia A. Temtamy, Mona S. Aglan, and Nagwa A. Meguid

9 Genetic Disorders in Ancient Egypt . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 273

Chahira Kozma

10 Genetic Diseases in Iraq . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 297

Hanan Ali Hamamy

11 Genetic Disorders in Jordan . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 325

Majed Dasouki and Hatem El-Shanti

12 Genetic Disorders in Kuwait . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 353

Nawal Makhseed

13 Genetic Disorders in Lebanon . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 377

Vazken M. Der Kaloustian

14 Genetic Disorders in Libya . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 443

Tawfeg Ben-Omran

15 Genetic Disorders in Morocco . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 455

Abdelaziz Sefiani

16 Genetic Disorders in Oman . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 473

Anna Rajab

17 Genetic Disorders Among the Palestinians . . . . . . . . . . . . . . . . . . . . . . . . . . . 491

Bassam Abu-Libdeh and Ahmad Said Teebi

18 Genetic Disorders in Qatar . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 515

Ahmad S. Teebi and Tawfeg Ben-Omran

19 Genetic Disorders in Saudi Arabia . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 531

Zuhair N. Al-Hassnan and Nadia Sakati

20 Genetic Disorders in Sudan . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 575

Mustafa A.M. Salih

21 Genetic Disorders in Tunisia . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 613

Elham Hassen and Lotfi Chouchane

xii Contents

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22 Genetic Disorders in the United Arab Emirates . . . . . . . . . . . . . . . . . . . . . 639

Lihadh Al-Gazali and Bassam R. Ali

23 Genetic Disorders Among Jews from Arab Countries . . . . . . . . . . . . . . . 677

Efrat Dagan and Ruth Gershoni-Baruch

Part V Cultural and Religious Attitudes Towards Genetic Issues

24 Prevention and Care of Genetic Disorders: An Islamic

Perspective . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 705

Aida I. Al Aqeel

25 Genetic Counseling in the Middle East . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 725

Shelley J. Kennedy and Muna Al-Saffar

Index . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 741

Contents xiii

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Contributors

Hasan Abdel Majeed Professor Emeritus of Pediatrics, University of Jordan,

Amman, Jordan

Bassam Abu-Libdeh Makassed Hospital & Al-Quds University, Jerusalem,

[email protected]

Mona S. Aglan Professor of Clinical Genetics, Clinical Genetics Department,

Human Genetics and Genome research division, National Research Centre, Cairo,

Egypt, [email protected]

Aida I. Al Aqeel Pediatrics, Medical Genetics and Endocrinology, Department of

Pediatrics, Riyadh Military Hospital, P. O. Box 7897, Riyadh 11159, Kingdom of

Saudi Arabia, [email protected], [email protected]

Stem Cell Therapy Program, King Faisal Specialist Hospital and Research Centre,

P. O. Box 3354, Riyadh 11211, Kingdom of Saudi Arabia

Lihadh Al-Gazali Department of Paediatrics, Faculty of Medicine and Health

Sciences, UAE University, Al-Ain, United Arab Emirates, [email protected]

Zuhair N. Al-Hassnan Associate Prof. of Genetics, College of Medicine, Alfaisal

University Consultant, Department of Medical Genetics, MBC-75, King Faisal

Specialist Hospital & Research Center, P.O. BOX 3354, Riyadh 11211, Saudi

Arabia, [email protected]

Bassam R. Ali Faculty of Medicine and Health Sciences, Department of

Pathology, UAE University, Al-Ain, United Arab Emirates

Sulayman S. Al-Qudsi Chief Economist and Head of Research Department-Arab

Bank, PLC. Amman-Jordan.Shaker bin Zeid Street, Shmeisani Area, 950545,

Amman, Jordan, [email protected]; [email protected]

Muna Al-Saffar Certified Genetic Counsellor, Children’s Hospital Boston, MA,

USA

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Project Manager, Dubai Harvard Foundation for Medical Research (DHFMR),

Dubai Health Care City, Dubai, United Arab Emirates

Tawfeg Ben-Omran Section of Clinical and Metabolic Genetics, Qatar Medical

Genetics Center, HamadMedical Corporation,Doha, Qatar, [email protected]

Alan H. Bittles Centre for Comparative Genomics, Murdoch University, South

Street, Perth, WA 6150, Australia, [email protected]

Lotfi Chouchane Professor of Genetic Medicine and Immunology, Genetic

Medicine Department, Weill Cornell Medical College, Qatar, loc2008@qatar-med.

cornell.edu

Efrat Dagan Institute of Human Genetics, RAMBAM Health Care Campus and

Department of Nursing, University of Haifa, Haifa, Israel

Majed Dasouki Professor of Pediatrics & Internal Medicine University of Kansas,

Kansas City, Kanasa, USA

VazkenM. Der Kaloustian Emeritus Professor of Pediatrics and HumanGenetics,

Mchill University, Montreal, Quebec, Canada, [email protected]

Hatem El-Shanti Director, Shafallah Medical Genetics Center, Doha, Qatar;

Adjunct Associate Professor of Pediatrics, University of Iowa, Iowa City, Iowa,

USA, [email protected]

Ruth Gershoni-Baruch Institute of Human Genetics, RAMBAM Health Care

Campus and the Ruth and Bruce Rappaport Faculty of Medicine, Technion-Insti-

tute of Technology, Haifa, Israel, [email protected]

Hanan A. Hamamy Department of Genetic Medicine and Development, Geneva

University Hospital, Geneva, Switzerland (formely Al-Mustansiriyah Medical

College, Baghdad, Iraq), [email protected]

Elham Hassen Molecular Immuno-Oncology Laboratory, Faculty of Medicine,

Monastir, Tunisia, [email protected]

Shelley J. Kennedy Certified Genetic Counsellor, Ontario Newborn Screening

Program & Regional Genetics Program, Children’s Hospital of Eastern Ontario,

Ottawa, ON, Canada, [email protected]

Chahira Kozma Department of Pediatrics, Georgetown University Hospital, 3800

Reservoir Rd N.W., Washington DC, USA, [email protected]; cck2@

gunet.georgetown.edu

Nawal Makhseed Department of Pediatrics, Jahra Hospital, Ministry of Health,

Kuwait, [email protected]

Samia A. Temtamy Professor of Human Genetics, Clinical Genetics Department,

Human Genetics and Genome, research division, National Research Centre, Cairo,

Egypt, [email protected]

xvi Contributors

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Anna Rajab Consultant Clinical Geneticist, Genetic Unit, Ministry of Health,

Sultanate of Oman, [email protected]

Amal A. Saadallah Medical College, Ain Shams University, Cairo, Egypt,

[email protected]

Nadia Sakati Consultant, Department of Pediatrics, MBC-58, King Faisal

Specialist Hospital & Research Center, P.O. BOX 3354, Riyadh 11211, Saudi

Arabia

Mustafa A.M. Salih Division of Pediatric Neurology, Department of Pediatrics,

College of Medicine, King Saud University, Riyadh, Saudi Arabia, mustafa_salih05

@yahoo.com; [email protected]

Abdelaziz Sefiani Department of Medical Genetics, National Institute of Heath/

University Mohammed V Souissi, Rabat 27, Avenue Ibn Batouta, BP 769, 11400,

Rabat, Morocco, [email protected]

Ahmad S. Teebi Weill Cornell Medical College, Qatar Foundation, Doha, Qatar,

[email protected]

Samia A. Temtamy Professor of Human Genetics, Clinical Genetics Department,

Human Genetics and Genome research division, National Research Centre, Cairo,

Egypt, [email protected]

Nagwa A. Meguid Profssor of Human Genetics, National Research Centre, Tahrir

street Dokki, Giza, Egypt, [email protected]

Contributors xvii

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