muscle diseases
TRANSCRIPT
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Supervised by:Dr.Eftekhar
Peresented by:Mohsen Koolivand
MSC Clinical of Biochemistry
Muscle Diseases
به نام خدا
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OutlineIntroduction
Marker of muscle damage
Muscle dystrophies
Metabolic myopathies
Other myopathies
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Introduction
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Marker of muscle damage
CK
Tree forms M-B-MM
CK-MB : Use of management of chest pain
The highest activities in : necrosis , Duchenne
Serial plasma CK : for myopathic and response to treatment
Normal plasma CK
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Other enzymes for marker
Aldolase , lactate dehydrogenase , myoglobin
In severe muscle damage, myoglobinuria can occur and cause a
brown colouration of the urine. Myoglobin can precipitate out in
the renal tubules and cause an obstructive nephropathy: the renal
failure associated with crush injuries is in part due to this.
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Muscle dystrophiesMuscular dystrophy (MD) is a broad term that describes a genetic (inherited)
disorder of the muscles. Muscular dystrophy causes the muscles in the body to
become very weak.
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Metabolic myopathies
Neuromuscular disorders in which the primary
symptom is muscle weakness due to dysfunction of
muscle fiber
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Inflammatory Myopathies Polymyositis Dermatomyositis Inclusion body myositis Viral
Muscular dystrophies Duchenne muscular Limb-girdle Congenital Fasioscapulohumeral Oculopharyngeal Emery – Dreifuss Distal (Welander)
Myotonic Syndromes Myotonic dystrophy Inherited Schwarz-Jampel Drug-induced
Congenital myopathies Central core disease Nemaline myopathy Myotubular Fiber-type disproportion
Metabolic myopathies Glycogenoses Mitochondrial Periodic paralysis
Endocrine myopathies Thyroid Parathyroid Adrenal/steroid Pituitary
Drug-induced/toxic
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15
Other myopathies
Myotonia
Myasthenia gravis
Lambert–Eaton myasthenic syndrome
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God is looking for clean hands and a pure heart