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Musculoskeletal tumors Soft tissue tumors

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Page 1: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Musculoskeletal tumors

Soft tissue tumors

Page 2: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Painless lump

Benign Malignant

Soft tissue tumorsin

Orthopedic practice

Connective tissues Blood vessels

1% of adult malignancies

Clinically very similar to benign tumors

Page 3: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

SizeLocationMobilityConsistencyMicrocirculatory status

X.RayBone scanC.T scanM.R.I

Needle Bx.Incisional Bx.Excisional Bx.

Page 4: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Low grade

High grade

With metastasis

I-a:Local wide resection

I-b:Wide amputation

II-a:Local radical resection

II-b:Radical amputation

?!Chemotherapy

Page 5: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Stopping growth

Continuous growth

Penetrating&infiltrating

Lipoma

Fibroma

Desmoid fibromatosis

Simple excision

Marginal excision

Local wide or radical

Page 6: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Low grade

I-a:Local wide resection

I-b:Wide amputation High gradeII-a:Local radical resection

II-b:Radical amputation

With metastasis?!

Chemotherapy

Page 7: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Malignant tumorsOf

Soft tissues 1% of adult malignancies

Clinically very similar to benign tumors MRI

Bx.

Needle or incisional

Never excisional

Local wide resectionLocal radical resection

Chemotherapy

Induction

Page 8: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Neurofibroma

Fibroma

Lipoma

Hemangioma

Desmoid fibromatosisMalignant fibrous histiocytosis

Fibrosarcoma

Synovial srcoma

Liposarcoma

Rhabdomyosarcoma

Page 9: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Neurofibroma

Soft&circumscribed

Rounded

Slightly tender

Skin or deeper tissues

Interstitial tissue of a periferal nerve

Solitary or Multiple

Spinal canal

Page 10: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Fibroma

Uncommon in extremities

Never in deep tissues

Firm,Round, painless nodule

Usually connected with a fascia or apponeurotic structure

Page 11: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Lipoma

Common

Almost any part

Usually subcutaneous

Soft,often large,lobulated,with thin capsule

Fat&Connective tissue

Local excision

Page 12: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

HemangiomaBirth

CapillaryCavernous Compressible

Cosmetic Thrombosis

Limb growth

Surgery Radiotherapy

Amputation

True Neoplasia

Hamartoma

Arterovenous malformation

RecurrenceWide resection

75-90%

Page 13: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Desmoid fibromatosis

RareYoung adult

Hard slow growing

Musculo-apponeurotic

Trunk&shoulder

Bx.”Fibro sarcoma

No metastasis

Local recurrence

Multicentric?!

Page 14: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Malignant fibrous histiocytosis

Commonest in olders

Local recurrence&metastasis

Page 15: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Fibrosarcoma

Localized Firm Round mass

Deeper tissues Neurofibromatosis

Pseudocapsule Infiltrating

Early lung metastasis

Page 16: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Synovial srcoma

Solid whitish fleshy mass

Insidious , but involving

Young or middle age adult

Wide resection AMPUTATION

Page 17: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Liposarcoma

Common Deep tissues

Lobulated mass

Buttock&Thigh

Enormous size

Prognosis ?!!

Radical excision

Amputation

Pleomorphic&Round cell

Mixoid tissue

RecMet

Page 18: Musculoskeletal tumors Soft tissue tumors Painless lump BenignMalignant Soft tissue tumors in Orthopedic practice Connective tissuesBlood vessels 1%

Rhabdomyosarcoma

Rare

Children & young adults

Trunk Lower limbs

Rapid growth

Early metastasis lung