paediatrics in picture
TRANSCRIPT
8/12/2019 Paediatrics in Picture
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PAEDIATRICS IN PICTURE
DR SANA BUSHRA
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STATION 1
• Identify the spot
• How many grades does
this condition have
• Name 3 diseases having
this condition
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ANSWER
• a)Clubbing
• b)Four grades
• Grade 1 fluctuation and softening of the nail bed
•Grade 2 obliteration of the normal angle between nailand nail bed
• Grade 3 convexity of the nail ; drum stick appearance
• Grade 4 broadened terminal pulp of the digit
• C) I ) tetralogy of fallot
• ii) celiac disease
• iii) cystic fibrosis
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STATION 2
• Identify
• Give five causes of this
condition
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ANSWER
• White pupillary reflex
• 1 Post infection congenital rubella
•
2 Galactosemia• 3 Retinoblastoma
• 4 Coat’s disease
• 5 Wilson disease
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STATION 3
• Name the spots
• Give ten causes
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ANSWER
• Café –au-lait spots
• 1 neurofibromatosis type 1 and 2
• 2 McCune Albright syndrome
• 3 ataxia telangiectasia
• 4 fanconi anemia• 5 Russell-silver syndrome
• 6 Tuberous sclerosis
• 7 Gaucher disease
• 8 Chediak – Higashi syndrome• 9 Turner syndrome
• 10 Proteus syndrome
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STATION 4
• Name the disease
• Name 10 complications
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ANSWER
• Measles
• 1 Giant cell pneumonia
• 2 Croup
• 3 Acute otitis media
• 4 activation of pulmonary TB• 5 diarrhea and vomiting
• 6 encephalitis
• 7 myocarditis
• 8 appendicitis• 9 hemmorraghic measles
• 10 subacute sclerosing panencephalitis
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STATION 5
• This chair has received
the attention of a 3
years old boy
• What is the diagnosis• Treatment
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ANSWER
• Pica
• Iron and calcium supplementation
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STATION 6
• Describe three features
shown in the picture
• What is the inheritance
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ANSWER
• 1 Depressed nasal bridge
• 2 Prominent maxilla
•
3 Prominent teeth• Inherited as autosomal recessive
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STATION 7
• Name the sign
• Name the condition
• Name an associated
syndrome
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ANSWER
• Double bubble sign
• Duodenal atresia
•
Down syndrome
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STATION 8
• Name the associated
lower limb abnormality
• What should the
mother have taken toavoid this
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ANSWER
• Pes cavus ( club feet )
• Folic acid
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STATION 9
• What do you see
• Give five differential
diagnosis
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ANSWER
• Periorbital bruising
• 1 leukemia
•
2 neuroblastoma ( results in raccoon eyes)• 3 basal skull fracture
• 4 bleeding disorder such as haemophilia
• 5 non accidental injury
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STATION 10
• This is an x ray of a 4year old boy whopresented with coarsefacies ,
hepatosplenomegalyand short stature
• Name the x ray findingshown
• Name four other x rayfindings
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ANSWER
• Bullet shaped metacarpals
• 1 oar shaped ribs
•
2 j shaped sella turcica• 3 beaking of the vertebra
• 4 thickened calvarium