proptosis from neurofibroma (kennerdell case 66)

Proptosis From Neurofibroma (Kennerdell Case 66)

John S. Kennerdell, MD

Chair, Department of Ophthalmology Allegheny General Hospital Professor, Ophthalmology

Drexel University College of Medicine

Case 66 - Slide 1/14

A 38-year-old man who was referred with chronic proptosis of the right eye with minimal visual disturbance. The proptosis measurements were 22 right and 18 left with a base of 106. There was no pain associated with the proptosis.


A café au lait spot on the patient’s skin indicating a patient with neurofibromatosis.


An axial CT scan of the irregular lesion in the superior right orbit with a variable internal consistency.


The lower axial view of the lesion in the region of the right optic nerve.


An unenhanced axial view of an MRI scan showing the lesion in the superior portion of the right orbit.


An unenhanced coronal MRI showing the lesion in the superior right orbit as a rounded lesion in the region of the superior rectus muscle.


The bony burr holes in the calvarium in the right frontal cranial orbitotomy being performed by a neurosurgeon.


The removal of the calvarium to gain access to the lesion in the superior right orbit.


The microscopic view of the reddish lesion in the superior right orbit.


A cryoprobe extracting the rounded irregular lesion from the superior right orbit.


The gross specimen of the solitary neurofibroma removed from the superior portion of the right orbit through the craniotomy.


The bony craniotomy site being replaced


The patient one month post-operatively with elimination of the right proptosis. He had no functional deficit.


An overhead view of the patient’s eyes showing the symmetry of the forward placement of both eyes.

proptosis from neurofibroma (kennerdell case 66)

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