rheumatic heart disease definition: streptococcal infection. children 5-15. pathology: - anti-gen...

23

Upload: cuthbert-carter

Post on 01-Jan-2016

225 views

Category:

Documents


1 download

TRANSCRIPT

Page 1: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical
Page 2: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Rheumatic Heart DiseaseDefinition: streptococcal infection. children 5-15.

•Pathology:- Anti-gen antibody reaction mediate

inflammation.

- * Clinical Feature;- Major Manifestation;

Cardiology [email protected] 2

Page 3: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

1- Carditis:- breatness- palpitation- chest pain.- 2- Polyarthritis- 3- Chorea:- 4-Erythema marginatum.

II. Minor Manifestation:Fever- Arthralgia-Raised ESR-

Leucocytosis- ASO

Cardiology [email protected] 3

Page 4: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

InvestigationInvestigation1-Evidence of systemic illness; Leucocytosis . ESR.2- Preceding streptococcal infection- Increase ASO. Child ---------- Adult---------- Throat Culture.

Cardiology [email protected] 4

Page 5: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

3- Carditis: X-ray: Cardiomegaly. ECG.: 1 st Heart block.

Treatment:-1.2 m pencillin\ bedrest\Aspirin\

corticosteriods\- 1.2 m pencillin monthly.

Cardiology [email protected] 5

Page 6: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Chronic Rheumatic Heart Chronic Rheumatic Heart DiseaseDisease

Chronic valvular heart disease develop in half of patient with rheumatic heart disease.

I.I. Mitral StenosisMitral Stenosis-Valve orifice by progressive fibrosis and

calcification of the valve leaflets and fusion of cusps.

-Blood flow Lt AP .pulmonary venous con- Dilatation of Lt atrium and ventricle.

Cardiology [email protected] 6

Page 7: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Clinical FeatureClinical FeatureSymptoms:Breathlessness-Fatigue- Odema-

Palpitation.Haemoptysis-

Signs:Signs:- Auscultation: Auscultation: loud 1st HS- MD murmer- Palpation: Shifted apex.

Cardiology [email protected] 7

Page 8: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

InvestigationInvestigation- ECG: Atrial Fabrilation.- X-ray: atrial enlargement.- Cardiac Cathetrization.

TreatmentTreatmentA- Medical :A- Medical :

B- Surgery.B- Surgery.

Cardiology [email protected] 8

Page 9: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

II. Mitral RegurgitationII. Mitral RegurgitationAbnormal leaking of blood through the mitral valveDysfunction of any valve part.

* Clinical Feature:* Clinical Feature:Symptoms: Dyspnea-Fatigue.Palpitation.Oedema.Ascitis.Signs:Apex shift- Pansystoloc murmer.

Cardiology [email protected] 9

Page 10: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

* Investigation:* Investigation:1- X-ray: enlarged lt atrium and ventricle.2- Echo: Dilated LA and LV.3- Dopller:4- Cardiac Catherterization.

ManagmentManagment

a)a)Medical : Medical : Diuretics,vasodilators.anticoagulant.antibioti

b)b)Surgical :Surgical :

Cardiology [email protected] 10

Page 11: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Aortic StenosisAortic Stenosis- Valvular heart disease caused by

incomplete opening of the valve.

- Causes:Causes:- Acquired: RF.- Congenital : bicusped aortic valve.

- * Clinical Feature:* Clinical Feature:- Mild and moderate are free.- Exertional dyspnea

Cardiology [email protected] 11

Page 12: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Angina.Extertional syncope .Sudden death.

• Signs:Signs:- Ejection systolic murmer.- Narrow pulse pressure.

*Investigation*Investigation:- ECG:Left ventricular hyperatrophty.- x-ray : enlarged left ventricle.

Cardiology [email protected] 12

Page 13: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Doppler : to detect the severity.

Treatment:Treatment:- Medical: B –blockers.- Surgical. - Aortic RegurgitationAortic Regurgitation- Leaking of the aortic valve.- Causes : in the valve cusps or root1- Congenital.2- Acquired:

Cardiology [email protected] 13

Page 14: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Pathology:Pathology:- Disease in the valve cusps: fibrosis and

fusion of the cusps retraction of the cusps.

- In the root: progressive dilatation of the root

- failure of the cusps to coapt.- * Clinical Picture: * Clinical Picture: Symptoms ( in sever cases) Brethnessness..Angina. Cardiology [email protected] 14

Page 15: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Signs:- Wide pulse presure.- Systolic murmer.- Crepitation .- 4th heart sound.

* Investigation:* Investigation:- ECG: inverted T wave.ECG: inverted T wave.- X-ray/X-ray/- Echo: dilated lt ventricle.Echo: dilated lt ventricle.- Catherterization.Catherterization.Cardiology [email protected] 15

Page 16: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Tricusped Stenosis:Tricusped Stenosis:-Causes.

• Clinical FeatureClinical FeatureSymptoms:Fatigue- Anarexia- peripheral odema.Signs:Raised jagular venous pressure.Mid diastolic murmer.

Cardiology [email protected] 16

Page 17: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

*Investigation*Investigation* Treatment:* Treatment:Medical : -Salt restriction.-Diuretics.Surgical:

Cardiology [email protected] 17

Page 18: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Tricusped RegurgitationTricusped Regurgitation Leaking of the tricusped valve commonly from functional dilatation of the Rt ventricle- or valvular damage.

Clinical Feature:Clinical Feature:Symptoms: oedema.abdominal pain

nausea.Signs: Ascitis.Anorexia.

*Treatment:*Treatment:- Relieving ventricular dilatation:-- If dilatation in the valve: annuloplasty ring.

Cardiology [email protected] 18

Page 19: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Pulmonary StenosisPulmonary Stenosis- In conginital,carcinoid syndrome.- * Clinical Feature:a) Symptoms- Usually free.- If sever: Exertional Dyspnea. Headness.b) Signs:Ejection click—Wide splitting of S2

Cardiology [email protected] 19

Page 20: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Investigation:Investigation:- ECG: Rt ven. Hyperatrophy.- X-ray.- Doppler.- Echo.

* Treatment:* Treatment:- Mild and moderate: noMild and moderate: no- Sever: Ballon Valvuplasty.Sever: Ballon Valvuplasty.- Valvotomy.Valvotomy.

Cardiology [email protected] 20

Page 21: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Pulmonary RegurgitationPulmonary Regurgitation- Rarely isolated..Usualy associated

with pulmonary artery dilatation due to pulmonary hypertension.

Clinical Feature:Clinical Feature:a)Symptoms:-- Symptomatic.- Symptoms appear with marked

increase in BP and RV failure:- Dyspnea on exertion--- OedemaCardiology [email protected] 21

Page 22: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Investigation1- x-ray: enlarged RV.2- Doppler:3- ECG.

*Treatment:*Treatment:I.Medical:-Supportive: treat RT ventricular failure.- Treat pulmonary dilatation.II. Surgical.

Cardiology [email protected] 22

Page 23: Rheumatic Heart Disease Definition: streptococcal infection. children 5-15. Pathology: - Anti-gen antibody reaction mediate inflammation. - * Clinical

Cardiology [email protected] 23