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  • 8/17/2019 Saq Discussion

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    Saq discussion

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    Qs

    • Outline anatomical defects andimaging ndings in – ASD

     – PDA

     – Coarctation of aorta

     – Mitral regurgitation

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    ASD

    • Commonest cong heart dx inadults (80!0"#

    •  a%normal o&ening in the atrialse&tum allo'ing communication%et'een the ) and *) atria

    • *t to t shunt – +f longstanding, -isenmenger

    &h.siolog. * shunt

    • /x more in

    •  ).&es – Ostium secundum1 80", interatrial

    connection at fossa o2alis

    ostium &rimum (assoc 'ith A3SD#

    Sinus 2enosus defect ( assoc PAP3D#

    4nrooofed coronar. sinus

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    • +maging

    • C5 – -nlarged rt atrium

    • ( ris6 throm%oem%oli,

    tach.ar.thmias#

     – -nlarged rt 2entricle• *aterallling

    retrosternal airs&ace

     –

     shunt 2ascularit.• Mar6ed central &ulm A

    dilatation, ma. %ecomeaneur.smal and calcif.

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    3SD

    •  defects inthe inter2entricular se&tumthat allo' a haemod.namiccommunication %et'eenthe ) and *) 2entricles

    • Commonest cong heart dxin childhood, onl. 70" inadults

    •  ).&es – Mem%ranous&erimem%ranous1

    80" – Muscular

    • +nlet

    • Outletsu%arterial

    • midmuscular

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    • indings – Shunt 2ascularit.

     – -nlargement of 3, *A and *3

     – left 2entricular a&ex &ro9ectsto the left, inferiorl. and&osteriorl.:

     – *A enlargement ;dou%ledensit. sign %ehind the rightatrium, and straightening orfocal con2exit. of the leftmediastinal %order is seen%elo' the &ulmonar. arter.

    shado': –

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    • cardiovascularassociationstetralog. of allot

    truncus arteriosus• dou%le outlet right

    2entricle

    • aortic coarctation

    • tricus&id atresia

    • aortic regurgitation

    • &ulmonar. stenosis

    http://radiopaedia.org/articles/tetralogy-of-fallot-tof-1http://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/double-outlet-right-ventriclehttp://radiopaedia.org/articles/double-outlet-right-ventriclehttp://radiopaedia.org/articles/coarctation-of-the-aortahttp://radiopaedia.org/articles/tricuspid-atresiahttp://radiopaedia.org/articles/missing?article%5Btitle%5D=aortic-regurgitationhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=aortic-regurgitationhttp://radiopaedia.org/articles/tricuspid-atresiahttp://radiopaedia.org/articles/tricuspid-atresiahttp://radiopaedia.org/articles/coarctation-of-the-aortahttp://radiopaedia.org/articles/coarctation-of-the-aortahttp://radiopaedia.org/articles/double-outlet-right-ventriclehttp://radiopaedia.org/articles/double-outlet-right-ventriclehttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/tetralogy-of-fallot-tof-1http://radiopaedia.org/articles/tetralogy-of-fallot-tof-1http://radiopaedia.org/articles/tetralogy-of-fallot-tof-1

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    PDA

    • &ersistent &atenc. of

    the ductus arteriosus anormal connection ofthe fetal circulation

    %et'een the aorta and the

    &ulmonar. arterial s.stemthat de2elo&s from the>th aortic arch:

    • Associations – Premature neonates

     – tetralog. of allot – -isenmenger s.ndrome

     – h.&o&lastic left heart

     – &ulmonar. atresia

     – Do'ns s.ndro

    http://radiopaedia.org/articles/tetralogy-of-fallot-tof-1http://radiopaedia.org/articles/eisenmenger-syndromehttp://radiopaedia.org/articles/hypoplastic-left-heart-syndromehttp://radiopaedia.org/articles/hypoplastic-left-heart-syndromehttp://radiopaedia.org/articles/hypoplastic-left-heart-syndromehttp://radiopaedia.org/articles/eisenmenger-syndromehttp://radiopaedia.org/articles/eisenmenger-syndromehttp://radiopaedia.org/articles/tetralogy-of-fallot-tof-1http://radiopaedia.org/articles/tetralogy-of-fallot-tof-1http://radiopaedia.org/articles/tetralogy-of-fallot-tof-1

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    • indings – Same as 3SD

    exce&t ma. ha2e

    enlarged ascendingand arch of aorta

     – Ductus ma. clacif.in adults

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    • Krichenko classifcation

    based on CT angiography• t.&e A? 8@" conical

    ductus,&rominent aorticam&ulla 'ith narro'ing at&ulmonar. arter. end

    • t.&e ? 'indo', short and 'ide

    ductus 'ith %lending of&ulmonar. arter.

    • t.&e C? long tu%ular ductus'ith no constrictions

    • t.&e D? multi&le constrictions

    'ith com&lex ductus• t.&e -? elongated ductus 'ith

    remote constriction

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    Coarctation• Coarctation of the aorta is

    a luminal narro'ing of a

    short section of the aortacommonl. at site ofinsertion of the ductusarteriosus

    • thought to de2elo& due to

    &resence of excessi2el.integrated ductal tissuearound the aortic isthmus,'hich contracts along 'iththe ductus arteriosus at

    the time of %irth:

    • +f se2ere, s.stemic&erfusion is com&romised'ith ductal closure

    • +f less se2ere,the %od.maintains &erfusion %.renal mechanisms,resulting in s.stemich.&ertension &roximal tothe coarctation: Collateralarterial 2essels de2elo&o2ertime to maintain lo'er%od. &erfusion as the

    &atientgro's

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    • the collateral

    &ath'a.s (internalmammar. and

    • &osteriormediastinalarteries

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    • associations – %icus&id aortic

    2al2e? B@80"

     –

    2entricular se&tal defect (3SD#

     – truncus arteriosus

     – trans&osition of the

     great arteries ()A#,#

     – mitral 2al2e defects

     – )urners s.ndrome7@0"

    http://radiopaedia.org/articles/bicuspid-aortic-valvehttp://radiopaedia.org/articles/bicuspid-aortic-valvehttp://radiopaedia.org/articles/bicuspid-aortic-valvehttp://radiopaedia.org/articles/ventricular-septal-defect-vsdhttp://radiopaedia.org/articles/ventricular-septal-defect-vsdhttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/transposition-of-the-great-arterieshttp://radiopaedia.org/articles/transposition-of-the-great-arterieshttp://radiopaedia.org/articles/transposition-of-the-great-arterieshttp://radiopaedia.org/articles/transposition-of-the-great-arterieshttp://radiopaedia.org/articles/transposition-of-the-great-arterieshttp://radiopaedia.org/articles/transposition-of-the-great-arterieshttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/truncus-arteriosushttp://radiopaedia.org/articles/ventricular-septal-defect-vsdhttp://radiopaedia.org/articles/ventricular-septal-defect-vsdhttp://radiopaedia.org/articles/ventricular-septal-defect-vsdhttp://radiopaedia.org/articles/bicuspid-aortic-valvehttp://radiopaedia.org/articles/bicuspid-aortic-valvehttp://radiopaedia.org/articles/bicuspid-aortic-valve

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    • CM or C) ma. %erequired &osto&erati2el. toesta%lish if there is recoarctation aneur.smaldilatation, or *3h.&ertro&h. secondar. toh.&ertension

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    Mitral regurgitation•  due to functional or

    anatomical d.sfunctionof the mitral 2al2e

    • acute causes – m.ocardial infarction

    'ith &a&illar. muscle

    ru&ture

     – chordal ru&ture (seen inm.xomatousdegeneration

     – infecti2e endocarditis

     – &rosthetic mitral 2al2ed.sfunction

    • Chronic causes – annular calcication

     – m.xomatousdegeneration

     – &re2ious

    infecti2einEammator. illness

     – rheumatic heartdisease

     – infecti2eendocarditis

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    indings

    • Marked Lt atriumenlargement – Con2exit.straightenin

    g lt heart order

     – Doule densit. sign

     – S&la.ing carina

     – Mild Lt ventricleenlargement

     –Moderate enlargedRV and pulm trunk 

     – Upper zone venousenlargement

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