congenital abnormalities (2)

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    CONGENITAL ABNORMALITIES

    OF GENITALIA MALE

    Oleh :

    Dr. Bakri B. Hasbulloh, SB.FINACS

    Ba!ia" Be#ah F$ %MS& RS%D $ab.$ara"!a"'ar

    Se"i" : () Ok*ober +))

    S%RA$ARTA

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    PATHOLOGY OF DISEASE :

    CONGENITAL

    TRAUMA

    INFECTION

    DEGENERATIVE

    / METABOLISMCANCER

    SURGERY INTERNIS PEDIATRIC

    OBGYNE / GYNECOLOGY THT

    SYARAF

    KULIT KELAMIN MATA

    RADIOLOGY PULMONOLOGY

    RM REPRODUCTIVE

    Dll.

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    FE"TILITY #$ I%FE"TILITY :

    CONGENITAL

    TRAUMA

    INFECTION

    DEGENERATIVE

    / METABOLISMCANCER

    COUPLE (PASANGAN SUAMI-ISTRI) CINTA ANAK FERTILE

    INFERTILE : AFTER MARRIED 1- YEARS NO CONTRACEPTION NORMAL SE!UAL NO BABY

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    I%FE"TILITY :

    pre testiculer

    testiculer

    post testiculer

    H"#$%&l&' *"#$+,

    %,%"

    #,"

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    Keli!! p" #ipot#l$us

    D,,"," LH FSH &%& GRH Keli!! p" #ipo%se

    I+"," *"#$+" $/0 %'$ &2"&"$#,&"

    Keli!! p" testiculer A$'&l" K$'$$' A$3*"' 4"l&%,&l G$&2$%$0" : ',0&

    #,'&%$5,," T&'& %,%" P,6&0"% "%,'"0 # DM. *"#,%," 2ll V&"0$0,l K"#%$3*"'

    K,l&"& #&3& %,%"0l, G&55& %$% #,'& : CBAVD K,l.5" 2& %'$%"l"%& #,'&

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    EMBR-OLOG- OF HE MALE

    ETERNAL GENITALIA

    NORMAL DEVELOPMENT : AT THE END of 2 weeks of development2 cell

    layes :

    T!e ectodem

    T!e P"m"t"ve #teak T!e Entodem

    $ T!e %loacal Mem&an $ T!e Alanto"s

    THE ME#ODERM

    $ T!e e'tenal (en"tal"a and an)s ae fomed &y developments

    a&o)t t!e cloacal mem&an and t!e allanto"s

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    Ab"or/ali*i*ies

    H*PO#PAD+A# AND %HORDAET!e )et!al meat)sOn t!e vental s)face of t! s!aft

    of t!e pen"s

    A laye of f"&o)s t"ss)e%HORDAE

    EP+#PAD+A# AND E,TROPH*

    T!e )et!al meat)s On t!e dosal s)face of t! s!aftof t!e pen"s

    T!e mem&ane ves"ca )"na"a defectE,TROPH*

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    A!to$il&0"

    1.ORGAN T,%" :

    T,%$%,$ S#,'&%$7$&

    E#"2"2"'" V&2,,, V,"3l& ,'"&l" P,"

    .PROSESSPERMATOGENESIS T4l

    ,'"",

    8.HORMON T,%$%,$

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    &I'OS'ADIA

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    &iposp"i !terior tipecoro!l

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    Masalah Hiosa#ia

    C%ASA : M%LTIFACTORIAL -enet"k

    Homonal

    Ras dll

    RE0ROD%$SI Pancaan spemato.oa

    SE$S%AL Pa"n

    %ROLOGI #tenos"s

    #t"ct)e

    #tone

    +#/ 0"nfeks" sal)an kenc"n(1

    URETHRA LETAK DI

    SEPAN9ANG PENISBUKAN DI TOPGLAND PENIS

    PANCARANABNORMAL

    PENIS MELENGKUNG DAN

    PENDEK

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    TI0E HI0OS0ADIA

    acat 034561 &edasakan letak ost")m )et!aekstena te&a(" 7 t"pe : T"pe (land

    Pat Ante"o

    8795;

    T"pe coonal

    T"pe pen"lPat Pen"l 3937;

    T"pe penoscotal

    Pat Poste"o

    2;

    T"pe pe"neal

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    THERA0-

    %HORDE%TOM* Meelease c!odaePen"s

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    1 0er*i/ba"!a" 0re Oera*i2e

    1. USIA Usi ( )ul! s$pi usi se)elu$ se*ol#

    +, TI'E &I'OS'ADIA-,

    BESAR 'ENIS., ADA TIDAKNA C&ORDAE

    BERHUBUNGAN

    DENGAN ONESTAGE OR TO

    STAGE OPERATIVE

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    COM'LICATION

    AERLY :BLEEDING

    INFECTION

    OEDEMA

    LATEFISTULE URETHRACUTANEUS

    REST CHORDAE

    STRICTURE URETHRAE

    STENOSIS URETHRAE

    DIVERTICLE URETHRAE

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    'ROGNOSIS

    COMMONL- : BAI$

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    3ASSALAAM%4ALAI$%M

    33