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Ewings sarcoma
BY DR. GIRIDHAR BOYAPATI PG DEPT. OF ORTHOPAEDICS
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Lab investigations
ESR is elevated WBC is elevated CRP is elevated. anemia is common lactic dehydrogenase
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Biopsy Gross appearance
may have liquid consistency mimicking pus.
Characteristic findings:
1.sheets of monotonous small round blue cells.
2.prominent nuclei and minimal cytoplasm.
3.may have
pseudorosettes (circle of cells with necrosis in center)
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DD
Small-round-cell tumor differential (by age)
< 5 yrs: Neuroblastoma or leukemia 5-10 yrs: Eosinophilic granuloma 5-30 yrs: Ewing's sarcoma >30 yrs: lymphoma > 50 yrs: myeloma
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Post-treatment considerations
Recurrence of primary disease is the major risk in the first 10 years after diagnosis.
A second malignancy occurs in approximately 1-2% of patients beginning 5 years after diagnosis; the most common second malignancy is Acute myeloid leukemia.
Therapeutic toxicities to the heart and kidneys, to the nervous and endocrine systems.
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