best cases of the airp · high grade liposarcoma of the inferior vena cava gunjan senapati, md beth...
TRANSCRIPT
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Best Cases of the AIRP
April 22 – May 17, 2013
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Musculoskeletal Best Case
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80-year-old man with history of ileal adenocarcinoma, status
post surgical resection and chemotherapy, presents with a
new mass in the left forearm.
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Myxoid Fibrosarcoma
Kyungmouk Steve Lee, MD
New York Presbyterian Hospital
New York, New York
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Neuroradiology Best Case
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12-year-old girl with no past medical history
presented with a single generalized seizure,
progressing to more frequent generalized
seizures and later developing complex partial
seizures despite medical therapy.
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Dysembryoplastic Neuroepithelial
Tumor
Adam Summerlin, MD
University of Colorado Health Science
Center
Aurora, Colorado
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Genitourinary Best Case
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66-year-old white man with family history
of renal cancer presented with
progressive urinary symptoms for the last
6 months.
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Renal Cell Carcinoma Associated
with Birt-Hogg-Dubé Syndrome
Bernardo Corrêa De Almeida Teixeira, MD
Hospital de Clínicas da Universidade
Federal do Paraná
Curitiba, Brazil
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PULMONARY AND MEDIASTINAL IMAGING
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57-year-old man with progressive weakness, 25
lb weight loss, hypokalemia, night sweats,
polyuria, and polydipsia.
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Bronchial Carcinoid (with ectopic ACTH production and bilateral
adrenal hyperplasia)
Deepa Sheth, MD
University of Chicago Hospitals
Chicago, Illinois
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Cardiovascular Imaging
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27-year-old man with inermittent abdominal
pain presents with extensive left lower
extremity deep venous thrombosis. No risk
factors, including negative
hypercoagulopathy.
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Head of pancreas is displaced anteriorly (purple arrow) by a mass expanding the IVC lumen (yellow arrows). Collateral
veins are present in retroperitoneum (green arrow).
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Coronal reformat contrast-enhanced CT reveals a heterogeneously enhancing mass expanding lumen of
inferior vena cava.
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Resected, expanded segment of
the inferior vena cava
(surface and cut cross sectional views)
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LEFT: Low-power H&E photomic shows sarcomatous cells filling the vessel lumen.
RIGHT: High-power H&E photomic shows multiple lipoblasts within the tumor.
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High Grade Liposarcoma of the Inferior
Vena Cava
Gunjan Senapati, MD
Beth Israel Deaconess Medical Center
Boston, Massachusetts
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Pediatric Best Case
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27-week gestation with abnormal
ultrasound.
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Cloacal Malformation
Cindy Fayard, MD
Hôpital Armand Trousseau
Paris, France
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Breast Best Case
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29-year-old woman in the postpartum period,
presenting with a large mass in the right breast.
She reported history of a hardened nodule in the
same area for the past 13 years, measuring about
3 cm, with marked growth during pregnancy. A
multilobulated tumor occupying almost the entire
right breast with skin ulceration was found on
physical examination.
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CC Views
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MLO Views
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Ultrasound
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MRI
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MRI Kinetics
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Gross Specimen
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Correlation
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Correlation
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Giant Complex Fibroadenoma
Bernardo Corrêa De Almeida Teixeira, MD
Hospital das Clínicas da Universidade
Federal do Paraná
Curitiba, Brazil
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Gastrointestinal Best Case
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34-year-old man from Saudi Arabia with past
medical history of end-stage renal disease status
post living unrelated kidney transplant in 2005
which subsequently failed, currently on dialysis for 7
months who recently flew to the United States for
evaluation of a liver mass and possible repeat
transplantation.
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Hepatic Arterial Phase Portal Venous Phase Equilibrium Phase
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T1 F/S T2 F/S
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H&E: bland
spindle cells mixed with
lymphocytes
EBER: positive
nuclear staining for
EBV-encoded RNA
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Epstein Barr Virus-Associated
Smooth Muscle Tumor
Andrew Chi, MD
Thomas Jefferson University Hospital
Philadelphia, Pennsylvania
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Many thanks to all of you for submitting
such great cases!
Have a safe trip home –
From the staff of the
American Institute for Radiologic Pathology