konjenital aortik ark
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TRANSCRIPT
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Dr. Devrim Ulaş URUTT.Ü.T.F. Radyodiagnostik A.D.
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NORMAL SOL AORTİK ARKGELİŞİMİ
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AORTİK ARK ANOMALİLERİ
• SAĞ ARK• ÇİFT ARK• SERVİKAL ARK• KOARKTASYON• INTERRUPTED AORTİK ARK• PSEUDOKOARKTASYON• ABERRANT SAĞ SUBKLAVYAN ARTER• PATENT DUKTUS ARTERIOSUS
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AORTİK ARK ANOMALİLERİORTAYA ÇIKIŞ ŞEKİLLERİ
• VASKULER RING– STRIDOR, WHEEZE, INFEKSİYON, DİSFAJİ
• KARDİYAK BOZUKLUKLARLA İLİŞKİLİ ORTAYA ÇIKAN
– SİYANOZ, KONJESTİV KALP YETMEZLİĞİ
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SAĞ AORTİK ARKEN SIK GÖRÜLEN TİPİ
• AYNA İMAJI
• ABERRAN SOL SUBKLAVYAN
• IZOLE SOL SUBKLAVYAN
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SAĞ AORTİK ARK
AYNA İMAJI
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AYNA IMAJI SAĞ AORTİK ARK
GELİŞİMİ
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ASEMPTOMATİK YETİŞKİNDE SAĞ AORTİK ARKAYNA İMAJI
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AYNA IMAJ SAĞ AORTİK ARK
• % 98 İNDE SİYANOTİK KALP HASTALIĞI
• TETRALOJİ, TRUNKUS, TRANSPOZİSYON,TRIKUSPID ATREZİSİ
• DAHA NADİR...VASKULAR RING VE KARDİYAK DEFEKT OLMAKSIZIN
• TRAKEA VE ÖZOFAGUSUN SAĞ TARAFINDA GİRİNTİ OLUŞUMU
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ABERRAN SOL SUBKLAVYANSAĞ AORTİK ARK
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ABERRAN SOL SUBKALVYEN ARTERSAĞ AORTİK ARK
GELİŞİMİ
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ABERRAN SOL SUBKALVYEN ARTERSAĞ AORTİK ARK
ASEMPTOMATİK YETİŞKİN
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ABERRAN SOL SUBKALVYEN ARTERSAĞ AORTİK ARK
ASEMPTOMATİK YETİŞKİN
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ABERRAN SOL SUBKALVYEN ARTERSAĞ AORTİK ARK
SOL SUBKALVYEN ARTER ANEVRİZMASI
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ABERRAN SOL SUBKALVYEN ARTERSAĞ AORTİK ARK
• EN SIK GÖRÜLEN TİPİDİR
• NADİREN SEMPTOMATİK OLUR• ÖZOFAGUS YADA TRAKEAYA AİT SEMPTOMLAR
• ÖZOFAGUS POSTERİORUNDA GİRİNTİ OLUŞUMU
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İZOLE SOL SUBKLAVYENSAĞ AORTİK ARK
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IZOLE SOL SUBKLAVYANSAĞ AORTİK ARK
GELİŞİMİ
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İZOLE SOL SUBKLAVYAN ARTERSAĞ AORTİK ARK
SOL KOL İSKEMİSİ SEMPTOMLARI VE İŞATRETLERİ
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İZOLE SOL SUBKLAVYAN SAĞ AORTİK ARK
• NADİREN KOL İSKEMİSİNE NEDEN OLUR
– NABIZDA AZALMA, YORGUNLUK, RAHATSIZLIK
• SUBKALVYAN ÇALMA SENDROMU
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ÇİFT AORTİK ARK
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ÇİFT AORTİK ARK GELİŞİMİ
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ÇİFT AORTİK ARKDİYAGRAM
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ÇİFT AORTİK ARKTEKRARLAYAN PNEUMONİLİ ÇOCUK OLGU
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ÇİFT AORTİK ARK DİSFAJİLİ ÇOCUK OLGU
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64 YAŞINDA KADIN HASTA MVA SONRASI ACİL BAŞVURU
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ASEMPTOMATİK YETİŞKİN
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ÇİFT AORTİK ARK
• EN SIK KOMPLET VASCKÜLER RING• STRIDOR, WHEEZİNG, ENFEKSİYON, DİSFAJİ
• KONJENİTAL KALP HASTALIKLARI DAHA NADİRDİR
• ÖZOFAGUSUN HER İKİ TARAFINA BASI
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SERVİKAL AORTİK ARK
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SERVİKAL AORTİK ARK
• SAĞ AORTİK ARK
• SOL AORTİK ARK
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SERVİKAL AORTİK ARK
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SERVİKAL ARKSAĞ SUBKLAVYAN (DİVERTİKÜLDEN)
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SAĞ SERVİKAL ARKABERRAN SOL SUBKLAVYAN ARTER
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SERVİKAL AORTİK ARK• GENELDE ASEMPTOMATİKTİR
• TRAKEA YADA ÖZOFAGUS KOMPRESYONU• WHEEZING, STRIDOR, ÖKSÜRÜK• BOĞULMA HİSSİ, REKURREN PNEUMONİ
• PALPABLE SUPRAKLAVIKULAR KİTLE
• KONJENİTAL KALP HASTALIĞI• TEF, VSD, PDA• DESSENDEN AORTADA KOARKTATASYON
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KOARKTASYON KONJENİTAL KALP HASTALIKLARININ % 5 i
• POSTDUKTAL • YETİŞKİN TİP
• DUKTUS YADA LİGAMENTUM ARTERİOSUMUN DİSTALİNDE KOARKTASYON
• JUXTADUCTAL • INFANT YADA ÇOCUKLARDA
• TRANSVERS AORTIİK ARK VE AORTİK ISTHMUSUN HİPOPLAZİSİ.
• AORTİK ARK INTERRUPSİYON• % 95 PDA, % 50 VSD İLE BERABER
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KOARKTASYON
• AORTİK TOPUZ • ŞEKİL 3 AORTİK TOPUZ
• DILATE ARTERLER• KOLLATERAL ARTERLER• SOL SUBKLAVYAN ARTER• ASSENDEN AORTA
• KOSTAL ÇENTİKLEŞME• SOL VENTRİKÜLDE
• HİPERTROFİ• DİLATASYON
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ŞEKİL 3 AORTİK TOPUZPRE VE POST STENOTİK DİLATASYON
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KOARKTASYON“ŞEKİL 3” AORTİK TOPUZ
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KOLLATERAL DAMARLAR
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KOARKTASYON
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KOARKTASYONSOL VENTRİKÜLER GENİŞLEME
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GÖĞÜS RADYOGRAMIDILATE SOL SUBKLAVYAN ARTER
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KOSTA ÇENTİĞİ
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W
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KOARKTASYON• AORTİK VALV
– MAJOR DEFORMASYON YADA BİKÜSPİT KAPAK
• % 10 SEREBRAL ANEVRMA İLE BERABER
• AORT DISSEKSİYONU
• İLİŞKİLİ ANOMALİLER– TURNER SYNDROME,
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10 YIL ÖNCE KOART.OPERASYONLU OLGUDA HEMOPTİZİ
AORTOBRONŞİAL FISTÜL
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ABERRAN
SAĞ SUBKLAVYAN ARTER
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ABERRAN SAĞ SUBKLAVYAN ARTERGELİŞİMİ
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ABERRAN SAĞ SUBKLAVYAN ARTER
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ABERRAN SAĞ SUBKLAVYAN ARTER
• TORAKSIN EN SIK GÖRÜLEN ARTERYEL ANOMALİSİ
• ÇOĞUNLUKLA İNSİDENTAL SAPTANIR• POSTERİOR ÖZOFAUSTA OBLİQ BASI OLUŞTURUR• DİĞER ANOMALİLERLE DE BERABER OLABİLİR
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ABERRAN SAĞ SUBKLAVYAN ARTER
AORTİK DISSEKSİYON
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LIGAMENTUM ARTERIOSUM
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BOVIN AORTİK ARK
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TEŞEKKÜRLER