margareta dahl lecture
TRANSCRIPT
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A cohort of children with myelomeningocele, born 2007- 2014:
Clinical characteristics Dahl M, Månsson E, Westbom L
Universities of Uppsala, Örebro and Lund, Sweden
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Decreased incidence at birth
MYELOMENINGOCELE
Increased survival rate into adulthood
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MMCUP Swedish National Quality Care Registry
Internet-based secondary prevention follow up
Spina Bifida and Hydrocephalus
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AIMS OF THE STUDY
Children with MMC, born 2007-2014
1. Clinical characteristics?
2. Different from children with MMC,
born 1988 - 1991?
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STUDY GROUP (23 children)
All children with MMC: * Born 2007-2014
* Uppsala/Örebro region
* Surgical closure
Medical records
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MMC born 2007-2014 (n = 23)
Boys 13 (56 %)
Prematurity 5 (22 %)
Sectio 20 (87 %)
Asphyxia 5 (22 %)
Thoracal cele 9 (39 %)
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MMC born 2007-2014 (n = 23)
Shunt 19 (83 %)
Severe spinal deform 10 (43 %)
Brainstem symptoms 8 (35 %)
Ad mortem < 1 mo 3 (13 %)
Ad mortem < 3 mo 4 (17 %)
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MMC born 2007-2014: Socio-demographic characteristics
Mother first generation immigrant 17 (74 %)
Single parent 6 (17 %)
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Prenatal diagnosis: 2007-2014
Early ultrasound 10
Late ultrasound 9
Not diagnosed 4
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COMPARISON GROUP
All children with MMC:
* Born 1988 - 1991
* Uppsala/Örebro region
* Surgical closure
22 children (9 boys)
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Children with MMC :
born 2007-2014 and 1988-1991
2007 1988 p
Mother immigrant 15/20 1/22 ***
Prenatal diagnosis 16/20 1/22 **
Early shunt 6/20 3/22 *
Ad mortem first mo 3/20 0/22
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CONCLUSIONS
Newborn children with MMC today: 1. Mother often first-generation immigrant!
2. Most often prenatally diagnosed!
3. Often severe medical complications!